| Type | MGI:General | Description | enteric neuronal intranuclear inclusions in numerous myenteric and submucosal ganglion cells; inclusions are positive for Atxn7 and Sumo1 about 50% of neurons in the distal ileum from 4 and 15 week old males contain inclusions loss of ganglion cells with Atxn7+ inclusions is not seen and the proportion of Atxn7+ inclusion-positive ChAT+ cells increases with age |