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Publication |
First Author: |
Kang R |
Year: |
2019 |
Journal: |
Front Synaptic Neurosci |
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Altered Regulation of Striatal Neuronal N-Methyl-D-Aspartate Receptor Trafficking by Palmitoylation in Huntington Disease Mouse Model. |
Volume: |
11 |
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Pages: |
3 |
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First Author: |
Qiu Z |
Year: |
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Journal: |
J Biol Chem |
Title: |
Sp1 is up-regulated in cellular and transgenic models of Huntington disease, and its reduction is neuroprotective. |
Volume: |
281 |
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Publication |
First Author: |
Cha MY |
Year: |
2018 |
Journal: |
PLoS Curr |
Title: |
Removal of the Mitochondrial Fission Factor Mff Exacerbates Neuronal Loss and Neurological Phenotypes in a Huntington's Disease Mouse Model. |
Volume: |
10 |
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Publication |
First Author: |
Sutton LM |
Year: |
2013 |
Journal: |
Hum Mol Genet |
Title: |
Hip14l-deficient mice develop neuropathological and behavioural features of Huntington disease. |
Volume: |
22 |
Issue: |
3 |
Pages: |
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Neurobiol Dis |
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2019 |
Journal: |
Proc Natl Acad Sci U S A |
Title: |
IKKβ slows Huntington's disease progression in R6/1 mice. |
Volume: |
116 |
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First Author: |
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Journal: |
Sci Signal |
Title: |
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Volume: |
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First Author: |
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Year: |
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Journal: |
J Neurosci |
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Striatal expression of a calmodulin fragment improved motor function, weight loss, and neuropathology in the R6/2 mouse model of Huntington's disease. |
Volume: |
29 |
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37 |
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2020 |
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Neurobiol Dis |
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Lentiviral delivery of human erythropoietin attenuates hippocampal atrophy and improves cognition in the R6/2 mouse model of Huntington's disease. |
Volume: |
144 |
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105024 |
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First Author: |
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2013 |
Journal: |
J Neurosci |
Title: |
MAP kinase phosphatase 1 (MKP-1/DUSP1) is neuroprotective in Huntington's disease via additive effects of JNK and p38 inhibition. |
Volume: |
33 |
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6 |
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Kannike K |
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J Biol Chem |
Title: |
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Volume: |
289 |
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Gong B |
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PLoS One |
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Volume: |
7 |
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7 |
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First Author: |
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J Clin Invest |
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Hum Mol Genet |
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Improvement of BDNF signalling by P42 peptide in Huntington's disease. |
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27 |
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First Author: |
Bichell TJV |
Year: |
2017 |
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Biochim Biophys Acta |
Title: |
Reduced bioavailable manganese causes striatal urea cycle pathology in Huntington's disease mouse model. |
Volume: |
1863 |
Issue: |
6 |
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First Author: |
Ekman FK |
Year: |
2019 |
Journal: |
Mol Ther Nucleic Acids |
Title: |
CRISPR-Cas9-Mediated Genome Editing Increases Lifespan and Improves Motor Deficits in a Huntington's Disease Mouse Model. |
Volume: |
17 |
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Biochim Biophys Acta |
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Hum Mol Genet |
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PLoS One |
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Biochem Biophys Res Commun |
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MicroRNA-124 targets CCNA2 and regulates cell cycle in STHdh(Q111)/Hdh(Q111) cells. |
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PLoS One |
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Intravitreal administration of HA-1077, a ROCK inhibitor, improves retinal function in a mouse model of huntington disease. |
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Nature |
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Cystathionine γ-lyase deficiency mediates neurodegeneration in Huntington's disease. |
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Biochim Biophys Acta |
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Enhancement of brain-type creatine kinase activity ameliorates neuronal deficits in Huntington's disease. |
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Pages: |
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Protein |
Organism: |
Mus musculus/domesticus |
Length: |
250
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Fragment?: |
true |
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Publication |
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Dysregulation of synaptic proteins, dendritic spine abnormalities and pathological plasticity of synapses as experience-dependent mediators of cognitive and psychiatric symptoms in Huntington's disease. |
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Uninterrupted CAG repeat drives striatum-selective transcriptionopathy and nuclear pathogenesis in human Huntingtin BAC mice. |
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•
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|
Protein |
Organism: |
Mus musculus/domesticus |
Length: |
483
|
Fragment?: |
false |
|
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•
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•
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Publication |
First Author: |
Wilson L |
Year: |
2005 |
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Genome Res |
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15 |
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8 |
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•
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Protein |
Organism: |
Mus musculus/domesticus |
Length: |
636
|
Fragment?: |
true |
|
•
•
•
•
•
|
Protein |
Organism: |
Mus musculus/domesticus |
Length: |
646
|
Fragment?: |
false |
|
•
•
•
•
•
|
Protein |
Organism: |
Mus musculus/domesticus |
Length: |
862
|
Fragment?: |
false |
|
•
•
•
•
•
|
Protein |
Organism: |
Mus musculus/domesticus |
Length: |
771
|
Fragment?: |
false |
|
•
•
•
•
•
|