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Search results 101 to 200 out of 646 for Fbn1

0.065s
Type Details Score
Publication
First Author: Sengle G
Year: 2012
Journal: PLoS Genet
Title: Microenvironmental regulation by fibrillin-1.
Volume: 8
Issue: 1
Pages: e1002425
Publication  
First Author: da Palma RK
Year: 2015
Journal: Respir Physiol Neurobiol
Title: Increased upper airway collapsibility in a mouse model of Marfan syndrome.
Volume: 207
Pages: 58-60
Publication
First Author: Syyong HT
Year: 2009
Journal: Br J Pharmacol
Title: Dysfunction of endothelial and smooth muscle cells in small arteries of a mouse model of Marfan syndrome.
Volume: 158
Issue: 6
Pages: 1597-608
Publication
First Author: Chung AW
Year: 2007
Journal: Br J Pharmacol
Title: Endothelial dysfunction and compromised eNOS/Akt signaling in the thoracic aorta during the progression of Marfan syndrome.
Volume: 150
Issue: 8
Pages: 1075-83
Publication
First Author: Gould RA
Year: 2012
Journal: PLoS One
Title: Multi-scale biomechanical remodeling in aging and genetic mutant murine mitral valve leaflets: insights into Marfan syndrome.
Volume: 7
Issue: 9
Pages: e44639
Publication
First Author: Mieremet A
Year: 2022
Journal: Sci Rep
Title: Endothelial dysfunction in Marfan syndrome mice is restored by resveratrol.
Volume: 12
Issue: 1
Pages: 22504
Publication  
First Author: Fernandes GR
Year: 2016
Journal: Sci Rep
Title: Identification of Loci Modulating the Cardiovascular and Skeletal Phenotypes of Marfan Syndrome in Mice.
Volume: 6
Pages: 22426
Publication
First Author: Pereira L
Year: 1997
Journal: Nat Genet
Title: Targetting of the gene encoding fibrillin-1 recapitulates the vascular aspect of Marfan syndrome.
Volume: 17
Issue: 2
Pages: 218-22
Publication
First Author: Guo G
Year: 2013
Journal: Aorta (Stamford)
Title: Indomethacin Prevents the Progression of Thoracic Aortic Aneurysm in Marfan Syndrome Mice.
Volume: 1
Issue: 1
Pages: 5-12
Publication
First Author: Kim KL
Year: 2014
Journal: Biomol Ther (Seoul)
Title: Analysis of disease progression-associated gene expression profile in fibrillin-1 mutant mice: new insight into molecular pathogenesis of marfan syndrome.
Volume: 22
Issue: 2
Pages: 143-8
Publication
First Author: Chen JZ
Year: 2019
Journal: Circ Rep
Title: Aortic Strain Correlates with Elastin Fragmentation in Fibrillin-1 Hypomorphic Mice.
Volume: 1
Issue: 5
Pages: 199-205
Publication
First Author: Bunton TE
Year: 2001
Journal: Circ Res
Title: Phenotypic alteration of vascular smooth muscle cells precedes elastolysis in a mouse model of Marfan syndrome.
Volume: 88
Issue: 1
Pages: 37-43
Publication
First Author: Lee JJ
Year: 2016
Journal: Ann Biomed Eng
Title: Losartan Attenuates Degradation of Aorta and Lung Tissue Micromechanics in a Mouse Model of Severe Marfan Syndrome.
Volume: 44
Issue: 10
Pages: 2994-3006
Publication
First Author: Zhou G
Year: 2000
Journal: In Vitro Cell Dev Biol Anim
Title: Partial cloning and sequencing of chick fibrillin-1 cDNA.
Volume: 36
Issue: 1
Pages: 19-25
Publication
First Author: McGaha T
Year: 2001
Journal: J Invest Dermatol
Title: Lack of skin fibrosis in tight skin (TSK) mice with targeted mutation in the interleukin-4R alpha and transforming growth factor-beta genes.
Volume: 116
Issue: 1
Pages: 136-43
Publication  
First Author: Gardi C
Year: 1994
Journal: Biochem J
Title: Neutrophil lysosomal dysfunctions in mutant C57 Bl/6J mice: interstrain variations in content of lysosomal elastase, cathepsin G and their inhibitors.
Volume: 299 ( Pt 1)
Pages: 237-45
Publication
First Author: Keil M
Year: 1996
Journal: Lab Invest
Title: A scanning electron microscopic investigation of genetic emphysema in tight-skin, pallid, and beige mice, three different C57 BL/6J mutants.
Volume: 74
Issue: 2
Pages: 353-62
Publication
First Author: Carta L
Year: 2006
Journal: J Biol Chem
Title: Fibrillins 1 and 2 perform partially overlapping functions during aortic development.
Volume: 281
Issue: 12
Pages: 8016-23
Publication
First Author: Li X
Year: 1993
Journal: Genomics
Title: Fibrillin genes map to regions of conserved mouse/human synteny on mouse chromosomes 2 and 18.
Volume: 18
Issue: 3
Pages: 667-72
Publication
First Author: Charbonneau NL
Year: 2010
Journal: J Biol Chem
Title: In vivo studies of mutant fibrillin-1 microfibrils.
Volume: 285
Issue: 32
Pages: 24943-55
Publication
First Author: Beene LC
Year: 2013
Journal: Invest Ophthalmol Vis Sci
Title: Nonselective assembly of fibrillin 1 and fibrillin 2 in the rodent ocular zonule and in cultured cells: implications for Marfan syndrome.
Volume: 54
Issue: 13
Pages: 8337-44
Publication
First Author: Carta L
Year: 2009
Journal: J Biol Chem
Title: p38 MAPK is an early determinant of promiscuous Smad2/3 signaling in the aortas of fibrillin-1 (Fbn1)-null mice.
Volume: 284
Issue: 9
Pages: 5630-6
Publication
First Author: Marque V
Year: 2001
Journal: Arterioscler Thromb Vasc Biol
Title: Aortic wall mechanics and composition in a transgenic mouse model of Marfan syndrome.
Volume: 21
Issue: 7
Pages: 1184-9
Publication
First Author: Calvi C
Year: 2013
Journal: PLoS Genet
Title: Hepatocyte growth factor, a determinant of airspace homeostasis in the murine lung.
Volume: 9
Issue: 2
Pages: e1003228
Publication
First Author: Sgonc R
Year: 1999
Journal: Arthritis Rheum
Title: Lack of endothelial cell apoptosis in the dermis of tight skin 1 and tight skin 2 mice.
Volume: 42
Issue: 3
Pages: 581-4
Publication
First Author: Griesenbach U
Year: 2008
Journal: Am J Respir Cell Mol Biol
Title: Validation of nasal potential difference measurements in gut-corrected CF knockout mice.
Volume: 39
Issue: 4
Pages: 490-6
Publication
First Author: Neptune ER
Year: 2003
Journal: Nat Genet
Title: Dysregulation of TGF-beta activation contributes to pathogenesis in Marfan syndrome.
Volume: 33
Issue: 3
Pages: 407-11
Publication  
First Author: Wang LW
Year: 2019
Journal: Matrix Biol
Title: Adamts10 inactivation in mice leads to persistence of ocular microfibrils subsequent to reduced fibrillin-2 cleavage.
Volume: 77
Pages: 117-128
Publication
First Author: Ng B
Year: 2023
Journal: Arterioscler Thromb Vasc Biol
Title: IL11 (Interleukin-11) Causes Emphysematous Lung Disease in a Mouse Model of Marfan Syndrome.
Volume: 43
Issue: 5
Pages: 739-754
Publication
First Author: Shi Y
Year: 2013
Journal: Invest Ophthalmol Vis Sci
Title: Development, composition, and structural arrangements of the ciliary zonule of the mouse.
Volume: 54
Issue: 4
Pages: 2504-15
Publication
First Author: Liu D
Year: 2014
Journal: J Am Soc Nephrol
Title: A Pkd1-Fbn1 genetic interaction implicates TGF-β signaling in the pathogenesis of vascular complications in autosomal dominant polycystic kidney disease.
Volume: 25
Issue: 1
Pages: 81-91
Publication
First Author: McKnite A
Year: 2023
Journal: Dev Dyn
Title: Lack of evidence that fibrillin1 regulates bone morphogenetic protein 4 activity in kidney or lung.
Volume: 252
Issue: 6
Pages: 761-769
Publication
First Author: Bhushan R
Year: 2019
Journal: J Cell Mol Med
Title: An integrative systems approach identifies novel candidates in Marfan syndrome-related pathophysiology.
Volume: 23
Issue: 4
Pages: 2526-2535
Publication
First Author: Chung AW
Year: 2007
Journal: Circ Res
Title: Loss of elastic fiber integrity and reduction of vascular smooth muscle contraction resulting from the upregulated activities of matrix metalloproteinase-2 and -9 in the thoracic aortic aneurysm in Marfan syndrome.
Volume: 101
Issue: 5
Pages: 512-22
Publication
First Author: Everett ET
Year: 1995
Journal: Comp Biochem Physiol A Physiol
Title: The role of mast cells in the development of skin fibrosis in tight-skin mutant mice.
Volume: 110
Issue: 2
Pages: 159-65
Publication
First Author: Matsushita Y
Year: 2007
Journal: J Immunol
Title: Intercellular adhesion molecule-1 deficiency attenuates the development of skin fibrosis in tight-skin mice.
Volume: 179
Issue: 1
Pages: 698-707
Publication
First Author: Oller J
Year: 2021
Journal: Circulation
Title: Extracellular Tuning of Mitochondrial Respiration Leads to Aortic Aneurysm.
Volume: 143
Issue: 21
Pages: 2091-2109
Publication
First Author: Li G
Year: 2020
Journal: J Clin Invest
Title: Chronic mTOR activation induces a degradative smooth muscle cell phenotype.
Volume: 130
Issue: 3
Pages: 1233-1251
Publication    
First Author: Mead TJ
Year: 2022
Journal: Elife
Title: Proteolysis of fibrillin-2 microfibrils is essential for normal skeletal development.
Volume: 11
Publication
First Author: Ong CJ
Year: 1999
Journal: Cell Immunol
Title: A role for T helper 2 cells in mediating skin fibrosis in tight-skin mice.
Volume: 196
Issue: 1
Pages: 60-8
Publication  
First Author: Bhattacharyya S
Year: 2016
Journal: Nat Commun
Title: Tenascin-C drives persistence of organ fibrosis.
Volume: 7
Pages: 11703
Publication
First Author: Hubmacher D
Year: 2015
Journal: Dis Model Mech
Title: Adamtsl2 deletion results in bronchial fibrillin microfibril accumulation and bronchial epithelial dysplasia--a novel mouse model providing insights into geleophysic dysplasia.
Volume: 8
Issue: 5
Pages: 487-99
Publication
First Author: Akiyama K
Year: 2012
Journal: Cell Stem Cell
Title: Mesenchymal-stem-cell-induced immunoregulation involves FAS-ligand-/FAS-mediated T cell apoptosis.
Volume: 10
Issue: 5
Pages: 544-55
Publication
First Author: Swank RT
Year: 1991
Journal: Blood
Title: Platelet storage pool deficiency associated with inherited abnormalities of the inner ear in the mouse pigment mutants muted and mocha.
Volume: 78
Issue: 8
Pages: 2036-44
Protein Coding Gene
Type: protein_coding_gene
Organism: Mus caroli
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: mouse, laboratory
Protein Coding Gene
Type: protein_coding_gene
Organism: Mus pahari
Protein Coding Gene
Type: protein_coding_gene
Organism: Mus spretus
Publication  
First Author: Wei F
Year: 2019
Journal: Cell Discov
Title: The Asprosin-OLFR734 hormonal signaling axis modulates male fertility.
Volume: 5
Pages: 55
Publication  
First Author: Liu Y
Year: 2020
Journal: Cell Discov
Title: The Asprosin-OLFR734 module regulates appetitive behaviors.
Volume: 6
Pages: 19
Publication
First Author: Yin W
Year: 1995
Journal: J Biol Chem
Title: Primary structure and developmental expression of Fbn-1, the mouse fibrillin gene.
Volume: 270
Issue: 4
Pages: 1798-806
Publication
First Author: Tsutsui K
Year: 2010
Journal: J Biol Chem
Title: ADAMTSL-6 is a novel extracellular matrix protein that binds to fibrillin-1 and promotes fibrillin-1 fibril formation.
Volume: 285
Issue: 7
Pages: 4870-82
Publication
First Author: Miao Y
Year: 2021
Journal: J Endocrinol
Title: Novel adipokine asprosin modulates browning and adipogenesis in white adipose tissue.
Volume: 249
Issue: 2
Pages: 83-93
Publication
First Author: Saito M
Year: 2011
Journal: J Biol Chem
Title: ADAMTSL6β protein rescues fibrillin-1 microfibril disorder in a Marfan syndrome mouse model through the promotion of fibrillin-1 assembly.
Volume: 286
Issue: 44
Pages: 38602-13
Publication
First Author: Charbonneau NL
Year: 2020
Journal: Anat Rec (Hoboken)
Title: Fibrillin-1 in the Vasculature: In Vivo Accumulation of eGFP-Tagged Fibrillin-1 in a Knockin Mouse Model.
Volume: 303
Issue: 6
Pages: 1590-1603
Publication
First Author: Smaldone S
Year: 2016
Journal: J Bone Miner Res
Title: Fibrillin-1 Regulates Skeletal Stem Cell Differentiation by Modulating TGFβ Activity Within the Marrow Niche.
Volume: 31
Issue: 1
Pages: 86-97
Publication  
First Author: Smaldone S
Year: 2016
Journal: Matrix Biol
Title: Fibrillin-1 microfibrils influence adult bone marrow hematopoiesis.
Volume: 52-54
Pages: 88-94
Publication
First Author: Schiavinato A
Year: 2016
Journal: J Invest Dermatol
Title: Targeting of EMILIN-1 and EMILIN-2 to Fibrillin Microfibrils Facilitates their Incorporation into the Extracellular Matrix.
Volume: 136
Issue: 6
Pages: 1150-60
Publication
First Author: Renard M
Year: 2017
Journal: PLoS One
Title: Sex, pregnancy and aortic disease in Marfan syndrome.
Volume: 12
Issue: 7
Pages: e0181166
Publication
First Author: Tehrani AY
Year: 2020
Journal: Sci Rep
Title: Characterization of doxycycline-mediated inhibition of Marfan syndrome-associated aortic dilation by multiphoton microscopy.
Volume: 10
Issue: 1
Pages: 7154
Publication
First Author: Verbrugghe P
Year: 2018
Journal: J Cardiovasc Pharmacol
Title: The Effect of a Nonpeptide Angiotensin II Type 2 Receptor Agonist, Compound 21, on Aortic Aneurysm Growth in a Mouse Model of Marfan Syndrome.
Volume: 71
Issue: 4
Pages: 215-222
Publication
First Author: Cui JZ
Year: 2019
Journal: Sci Rep
Title: In vivo characterization of doxycycline-mediated protection of aortic function and structure in a mouse model of Marfan syndrome-associated aortic aneurysm.
Volume: 9
Issue: 1
Pages: 2071
Publication
First Author: Matt P
Year: 2009
Journal: Circulation
Title: Circulating transforming growth factor-beta in Marfan syndrome.
Volume: 120
Issue: 6
Pages: 526-32
Publication
First Author: Rodríguez-Rovira I
Year: 2022
Journal: Free Radic Biol Med
Title: Allopurinol blocks aortic aneurysm in a mouse model of Marfan syndrome via reducing aortic oxidative stress.
Volume: 193
Issue: Pt 2
Pages: 538-550
Publication
First Author: Cavanaugh NB
Year: 2017
Journal: Ann Thorac Surg
Title: A Novel Murine Model of Marfan Syndrome Accelerates Aortopathy and Cardiomyopathy.
Volume: 104
Issue: 2
Pages: 657-665
Publication
First Author: Franken R
Year: 2014
Journal: PLoS One
Title: No beneficial effect of general and specific anti-inflammatory therapies on aortic dilatation in Marfan mice.
Volume: 9
Issue: 9
Pages: e107221
Publication
First Author: Habashi JP
Year: 2006
Journal: Science
Title: Losartan, an AT1 antagonist, prevents aortic aneurysm in a mouse model of Marfan syndrome.
Volume: 312
Issue: 5770
Pages: 117-21
Publication
First Author: Yang HH
Year: 2009
Journal: Br J Pharmacol
Title: Long-term effects of losartan on structure and function of the thoracic aorta in a mouse model of Marfan syndrome.
Volume: 158
Issue: 6
Pages: 1503-12
Publication  
First Author: Saddic L
Year: 2023
Journal: Int J Mol Sci
Title: 17 β-Estradiol Impedes Aortic Root Dilation and Rupture in Male Marfan Mice.
Volume: 24
Issue: 17
Publication
First Author: Mas-Stachurska A
Year: 2021
Journal: Sci Rep
Title: Postsystolic thickening is a potential new clinical sign of injured myocardium in marfan syndrome.
Volume: 11
Issue: 1
Pages: 15790
Publication
First Author: Emrich F
Year: 2019
Journal: J Cell Mol Med
Title: Anatomically specific reactive oxygen species production participates in Marfan syndrome aneurysm formation.
Volume: 23
Issue: 10
Pages: 7000-7009
Publication
First Author: Roohi J
Year: 2017
Journal: J Nutr
Title: Moderately Elevated Homocysteine Does Not Contribute to Thoracic Aortic Aneurysm in Mice.
Volume: 147
Issue: 7
Pages: 1290-1295
Publication
First Author: Campens L
Year: 2015
Journal: Pediatr Res
Title: Intrinsic cardiomyopathy in Marfan syndrome: results from in-vivo and ex-vivo studies of the Fbn1C1039G/+ model and longitudinal findings in humans.
Volume: 78
Issue: 3
Pages: 256-63
Publication
First Author: Tae HJ
Year: 2016
Journal: Am J Physiol Heart Circ Physiol
Title: Cardiac remodeling in the mouse model of Marfan syndrome develops into two distinctive phenotypes.
Volume: 310
Issue: 2
Pages: H290-9
Publication
First Author: Sato T
Year: 2018
Journal: J Am Heart Assoc
Title: Statins Reduce Thoracic Aortic Aneurysm Growth in Marfan Syndrome Mice via Inhibition of the Ras-Induced ERK (Extracellular Signal-Regulated Kinase) Signaling Pathway.
Volume: 7
Issue: 21
Pages: e008543
Publication  
First Author: Okamura H
Year: 2017
Journal: Physiol Rep
Title: Long-term miR-29b suppression reduces aneurysm formation in a Marfan mouse model.
Volume: 5
Issue: 8
Publication
First Author: Cook JR
Year: 2015
Journal: Arterioscler Thromb Vasc Biol
Title: Dimorphic effects of transforming growth factor-β signaling during aortic aneurysm progression in mice suggest a combinatorial therapy for Marfan syndrome.
Volume: 35
Issue: 4
Pages: 911-7
Publication
First Author: Uriarte JJ
Year: 2016
Journal: PLoS One
Title: Early Impairment of Lung Mechanics in a Murine Model of Marfan Syndrome.
Volume: 11
Issue: 3
Pages: e0152124
Publication    
First Author: Doyle JJ
Year: 2015
Journal: Elife
Title: A deleterious gene-by-environment interaction imposed by calcium channel blockers in Marfan syndrome.
Volume: 4
Publication
First Author: Merk DR
Year: 2012
Journal: Circ Res
Title: miR-29b participates in early aneurysm development in Marfan syndrome.
Volume: 110
Issue: 2
Pages: 312-24
Publication
First Author: Perrotta P
Year: 2020
Journal: Arterioscler Thromb Vasc Biol
Title: Partial Inhibition of Glycolysis Reduces Atherogenesis Independent of Intraplaque Neovascularization in Mice.
Volume: 40
Issue: 5
Pages: 1168-1181
Publication
First Author: White Z
Year: 2019
Journal: Am J Pathol
Title: Sildenafil Prevents Marfan-Associated Emphysema and Early Pulmonary Artery Dilation in Mice.
Volume: 189
Issue: 8
Pages: 1536-1546
Publication
First Author: de la Fuente-Alonso A
Year: 2021
Journal: Nat Commun
Title: Aortic disease in Marfan syndrome is caused by overactivation of sGC-PRKG signaling by NO.
Volume: 12
Issue: 1
Pages: 2628
Publication  
First Author: Hibender S
Year: 2019
Journal: Cardiovasc Pathol
Title: Renal cystic disease in the Fbn1C1039G/+ Marfan mouse is associated with enhanced aortic aneurysm formation.
Volume: 38
Pages: 1-6
Publication
First Author: Gibson C
Year: 2017
Journal: J Appl Physiol (1985)
Title: Mild aerobic exercise blocks elastin fiber fragmentation and aortic dilatation in a mouse model of Marfan syndrome associated aortic aneurysm.
Volume: 123
Issue: 1
Pages: 147-160