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Search results 201 to 300 out of 732 for Cftr

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Category: Publication
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Type Details Score
Publication
20570219 | J:233126
First Author: Paradis J
Year: 2010
Journal: J Cyst Fibros
Title: Osteopenia in Cftr-deltaF508 mice.
Volume: 9
Issue: 4
Pages: 239-45
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Publication
7560099 | J:29074
First Author: Zeiher BG
Year: 1995
Journal: J Clin Invest
Title: A mouse model for the delta F508 allele of cystic fibrosis.
Volume: 96
Issue: 4
Pages: 2051-64
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Publication
20478977 | J:176765
First Author: Muchekehu RW
Year: 2010
Journal: J Physiol
Title: A new role for bicarbonate secretion in cervico-uterine mucus release.
Volume: 588
Issue: Pt 13
Pages: 2329-42
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Publication
23269368 | J:232013
First Author: Sellers ZM
Year: 2013
Journal: J Cyst Fibros
Title: Left ventricular and aortic dysfunction in cystic fibrosis mice.
Volume: 12
Issue: 5
Pages: 517-24
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Publication
24373976 | J:323177
First Author: Bazett M
Year: 2014
Journal: J Cyst Fibros
Title: Airway hyperresponsiveness in FVB/N delta F508 cystic fibrosis transmembrane conductance regulator mice.
Volume: 13
Issue: 4
Pages: 378-83
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Publication
11978765 | J:133160
First Author: Oceandy D
Year: 2002
Journal: Hum Mol Genet
Title: Gene complementation of airway epithelium in the cystic fibrosis mouse is necessary and sufficient to correct the pathogen clearance and inflammatory abnormalities.
Volume: 11
Issue: 9
Pages: 1059-67
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Publication
38870301 | J:359278
First Author: Sun Y
Year: 2024
Journal: Science
Title: In vivo editing of lung stem cells for durable gene correction in mice.
Volume: 384
Issue: 6701
Pages: 1196-1202
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Publication
1284640 | J:23857
First Author: Whitsett JA
Year: 1992
Journal: Nat Genet
Title: Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice.
Volume: 2
Issue: 1
Pages: 13-20
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Publication
9613608 | J:47599
First Author: Wang S
Year: 1998
Journal: FEBS Lett
Title: Peptide binding consensus of the NHE-RF-PDZ1 domain matches the C-terminal sequence of cystic fibrosis transmembrane conductance regulator (CFTR).
Volume: 427
Issue: 1
Pages: 103-8
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Publication
15064229 | J:102142
First Author: Kaur S
Year: 2004
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Acidic duodenal pH alters gene expression in the cystic fibrosis mouse pancreas.
Volume: 287
Issue: 2
Pages: G480-90
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Publication
22859830 | J:189685
First Author: Bonfield TL
Year: 2012
Journal: J Leukoc Biol
Title: Absence of the cystic fibrosis transmembrane regulator (Cftr) from myeloid-derived cells slows resolution of inflammation and infection.
Volume: 92
Issue: 5
Pages: 1111-22
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Publication
7537458 | J:24488
First Author: De Lisle RC
Year: 1995
Journal: Am J Physiol
Title: Increased expression of sulfated gp300 and acinar tissue pathology in pancreas of CFTR(-/-) mice.
Volume: 268
Issue: 4 Pt 1
Pages: G717-23
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Publication
1720548 | J:2356
First Author: Koller BH
Year: 1991
Journal: Proc Natl Acad Sci U S A
Title: Toward an animal model of cystic fibrosis: targeted interruption of exon 10 of the cystic fibrosis transmembrane regulator gene in embryonic stem cells.
Volume: 88
Issue: 23
Pages: 10730-4
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Publication
19633071 | J:154224
First Author: Vandivier RW
Year: 2009
Journal: Am J Physiol Lung Cell Mol Physiol
Title: Dysfunctional cystic fibrosis transmembrane conductance regulator inhibits phagocytosis of apoptotic cells with proinflammatory consequences.
Volume: 297
Issue: 4
Pages: L677-86
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Publication
25271146 | J:219840
First Author: Pfister S
Year: 2015
Journal: J Comp Neurol
Title: Novel role of cystic fibrosis transmembrane conductance regulator in maintaining adult mouse olfactory neuronal homeostasis.
Volume: 523
Issue: 3
Pages: 406-30
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Publication
16804061 | J:111876
First Author: Stalvey MS
Year: 2006
Journal: Diabetes
Title: Cystic fibrosis transmembrane conductance regulator deficiency exacerbates islet cell dysfunction after beta-cell injury.
Volume: 55
Issue: 7
Pages: 1939-45
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Publication
23239501 | J:205088
First Author: Xu Y
Year: 2013
Journal: Am J Respir Cell Mol Biol
Title: Low sphingosine-1-phosphate impairs lung dendritic cells in cystic fibrosis.
Volume: 48
Issue: 2
Pages: 250-7
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Publication
23986201 | J:210203
First Author: Collaco AM
Year: 2013
Journal: Am J Physiol Cell Physiol
Title: Functional vacuolar ATPase (V-ATPase) proton pumps traffic to the enterocyte brush border membrane and require CFTR.
Volume: 305
Issue: 9
Pages: C981-96
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Publication
18790990 | J:142605
First Author: Manson ME
Year: 2008
Journal: Am J Physiol Lung Cell Mol Physiol
Title: cAMP-mediated regulation of cholesterol accumulation in cystic fibrosis and Niemann-Pick type C cells.
Volume: 295
Issue: 5
Pages: L809-19
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Publication
21625623 | J:172718
First Author: Xu WM
Year: 2011
Journal: PLoS One
Title: Defective CFTR-dependent CREB activation results in impaired spermatogenesis and azoospermia.
Volume: 6
Issue: 5
Pages: e19120
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Publication
15289377 | J:102151
First Author: Chen H
Year: 2004
Journal: Circulation
Title: Targeted inactivation of cystic fibrosis transmembrane conductance regulator chloride channel gene prevents ischemic preconditioning in isolated mouse heart.
Volume: 110
Issue: 6
Pages: 700-4
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Publication
11404242 | J:107842
First Author: Velsor LW
Year: 2001
Journal: Am J Physiol Lung Cell Mol Physiol
Title: Antioxidant imbalance in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice.
Volume: 281
Issue: 1
Pages: L31-8
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Publication
22135344 | J:323171
First Author: Chaudhary N
Year: 2012
Journal: Am J Respir Crit Care Med
Title: Cystic fibrosis transmembrane conductance regulator regulates epithelial cell response to Aspergillus and resultant pulmonary inflammation.
Volume: 185
Issue: 3
Pages: 301-10
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Publication
16418321 | J:108346
First Author: Guilbault C
Year: 2006
Journal: Physiol Genomics
Title: Distinct pattern of lung gene expression in the Cftr-KO mice developing spontaneous lung disease compared with their littermate controls.
Volume: 25
Issue: 2
Pages: 179-93
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Publication
9835624 | J:51326
First Author: Marvão P
Year: 1998
Journal: J Clin Invest
Title: Cl- absorption across the thick ascending limb is not altered in cystic fibrosis mice. A role for a pseudo-CFTR Cl- channel.
Volume: 102
Issue: 11
Pages: 1986-93
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12482874 | J:107360
First Author: Xu Y
Year: 2003
Journal: J Biol Chem
Title: Transcriptional adaptation to cystic fibrosis transmembrane conductance regulator deficiency.
Volume: 278
Issue: 9
Pages: 7674-82
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Publication
9124365 | J:38820
First Author: Grubb BR
Year: 1997
Journal: Am J Physiol
Title: Enhanced colonic Na+ absorption in cystic fibrosis mice versus normal mice.
Volume: 272
Issue: 2 Pt 1
Pages: G393-400
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9387959 | J:44572
First Author: Cowley EA
Year: 1997
Journal: Eur Respir J
Title: Mucociliary clearance in cystic fibrosis knockout mice infected with Pseudomonas aeruginosa.
Volume: 10
Issue: 10
Pages: 2312-8
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Publication
18450781 | J:176394
First Author: Bonvin E
Year: 2008
Journal: J Physiol
Title: Congenital tracheal malformation in cystic fibrosis transmembrane conductance regulator-deficient mice.
Volume: 586
Issue: 13
Pages: 3231-43
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Publication
7533607 | J:25032
First Author: Snouwaert JN
Year: 1995
Journal: Am J Respir Crit Care Med
Title: A murine model of cystic fibrosis.
Volume: 151
Issue: 3 Pt 2
Pages: S59-64
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Publication
10615064 | J:59774
First Author: Steagall WK
Year: 2000
Journal: Am J Respir Cell Mol Biol
Title: Cystic fibrosis transmembrane conductance regulator-dependent regulation of epithelial inducible nitric oxide synthase expression.
Volume: 22
Issue: 1
Pages: 45-50
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Publication
11942920 | J:127847
First Author: Praetorius J
Year: 2002
Journal: Acta Physiol Scand
Title: The cystic fibrosis transmembrane conductance regulator is not a base transporter in isolated duodenal epithelial cells.
Volume: 174
Issue: 4
Pages: 327-36
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8875228 | J:36166
First Author: Dorin JR
Year: 1996
Journal: Gene Ther
Title: A demonstration using mouse models that successful gene therapy for cystic fibrosis requires only partial gene correction.
Volume: 3
Issue: 9
Pages: 797-801
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17873061 | J:125319
First Author: Ostedgaard LS
Year: 2007
Journal: Proc Natl Acad Sci U S A
Title: Processing and function of CFTR-DeltaF508 are species-dependent.
Volume: 104
Issue: 39
Pages: 15370-5
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27313231 | J:292898
First Author: Knauf F
Year: 2017
Journal: J Am Soc Nephrol
Title: Loss of Cystic Fibrosis Transmembrane Regulator Impairs Intestinal Oxalate Secretion.
Volume: 28
Issue: 1
Pages: 242-249
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Publication
17290033 | J:136608
First Author: Lindert J
Year: 2007
Journal: Am J Respir Cell Mol Biol
Title: Chloride-dependent secretion of alveolar wall liquid determined by optical-sectioning microscopy.
Volume: 36
Issue: 6
Pages: 688-96
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7534985 | J:23936
First Author: Leung AY
Year: 1995
Journal: Am J Physiol
Title: cAMP- but not Ca(2+)-regulated Cl- conductance in the oviduct is defective in mouse model of cystic fibrosis.
Volume: 268
Issue: 3 Pt 1
Pages: C708-12
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16763223 | J:126889
First Author: Velsor LW
Year: 2006
Journal: Am J Respir Cell Mol Biol
Title: Mitochondrial oxidative stress in the lungs of cystic fibrosis transmembrane conductance regulator protein mutant mice.
Volume: 35
Issue: 5
Pages: 579-86
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Publication
18054564 | J:135618
First Author: Young FD
Year: 2007
Journal: Gastroenterology
Title: Amelioration of cystic fibrosis intestinal mucous disease in mice by restoration of mCLCA3.
Volume: 133
Issue: 6
Pages: 1928-37
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Publication
15064232 | J:95677
First Author: Blanco PG
Year: 2004
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Induction of colitis in cftr-/- mice results in bile duct injury.
Volume: 287
Issue: 2
Pages: G491-6
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14739145 | J:95681
First Author: Norkina O
Year: 2004
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Inflammation of the cystic fibrosis mouse small intestine.
Volume: 286
Issue: 6
Pages: G1032-41
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12164788 | J:79985
First Author: Thomsson KA
Year: 2002
Journal: Biochem J
Title: Intestinal mucins from cystic fibrosis mice show increased fucosylation due to an induced Fucalpha1-2 glycosyltransferase.
Volume: 367
Issue: Pt 3
Pages: 609-16
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Publication
16740913 | J:200888
First Author: Jin R
Year: 2006
Journal: J Med Genet
Title: The cystic fibrosis transmembrane conductance regulator (Cftr) modulates the timing of puberty in mice.
Volume: 43
Issue: 6
Pages: e29
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12461646 | J:80597
First Author: Haston CK
Year: 2002
Journal: Mamm Genome
Title: Mapping of genetic factors influencing the weight of cystic fibrosis knockout mice.
Volume: 13
Issue: 11
Pages: 614-8
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Publication
18325992 | J:145380
First Author: Hodges CA
Year: 2008
Journal: Endocrinology
Title: Infertility in females with cystic fibrosis is multifactorial: evidence from mouse models.
Volume: 149
Issue: 6
Pages: 2790-7
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Publication
16455659 | J:112698
First Author: Xu Y
Year: 2006
Journal: J Biol Chem
Title: Functional genomic responses to cystic fibrosis transmembrane conductance regulator (CFTR) and CFTR(delta508) in the lung.
Volume: 281
Issue: 16
Pages: 11279-91
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Publication
29423078 | J:321497
First Author: Yang X
Year: 2018
Journal: Oncotarget
Title: Molecular mechanisms of calcium signaling in the modulation of small intestinal ion transports and bicarbonate secretion.
Volume: 9
Issue: 3
Pages: 3727-3740
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26709821 | J:239988
First Author: Deschemin JC
Year: 2015
Journal: PLoS One
Title: Iron Homeostasis and Inflammatory Status in Mice Deficient for the Cystic Fibrosis Transmembrane Regulator.
Volume: 10
Issue: 12
Pages: e0145685
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Publication
26683699 | J:239996
First Author: Xie C
Year: 2016
Journal: FASEB J
Title: Mechanosensitivity of wild-type and G551D cystic fibrosis transmembrane conductance regulator (CFTR) controls regulatory volume decrease in simple epithelia.
Volume: 30
Issue: 4
Pages: 1579-89
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Publication
14977953 | J:88586
First Author: van Heeckeren AM
Year: 2004
Journal: Infect Immun
Title: Nutritional effects on host response to lung infections with mucoid Pseudomonas aeruginosa in mice.
Volume: 72
Issue: 3
Pages: 1479-86
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28394330 | J:256459
First Author: Romani L
Year: 2017
Journal: Nat Med
Title: Thymosin α1 represents a potential potent single-molecule-based therapy for cystic fibrosis.
Volume: 23
Issue: 5
Pages: 590-600
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34830048 | J:315032
 
First Author: Bacci G
Year: 2021
Journal: Int J Mol Sci
Title: Lung and Gut Microbiota Changes Associated with Pseudomonas aeruginosa Infection in Mouse Models of Cystic Fibrosis.
Volume: 22
Issue: 22
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Publication
18006890 | J:323253
First Author: Haston CK
Year: 2008
Journal: Am J Respir Crit Care Med
Title: Persistent osteopenia in adult cystic fibrosis transmembrane conductance regulator-deficient mice.
Volume: 177
Issue: 3
Pages: 309-15
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Publication
22287709 | J:181250
First Author: Bazett M
Year: 2012
Journal: J Immunol
Title: Strain-dependent airway hyperresponsiveness and a chromosome 7 locus of elevated lymphocyte numbers in cystic fibrosis transmembrane conductance regulator-deficient mice.
Volume: 188
Issue: 5
Pages: 2297-304
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Publication
35413967 | J:323271
First Author: da Cunha MF
Year: 2022
Journal: Sci Rep
Title: Systemic bis-phosphinic acid derivative restores chloride transport in Cystic Fibrosis mice.
Volume: 12
Issue: 1
Pages: 6132
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32528461 | J:323260
 
First Author: Isopi E
Year: 2020
Journal: Front Immunol
Title: Resolvin D1 Reduces Lung Infection and Inflammation Activating Resolution in Cystic Fibrosis.
Volume: 11
Pages: 581
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11390493 | J:128660
First Author: Schroeder TH
Year: 2001
Journal: J Immunol
Title: Transgenic cystic fibrosis mice exhibit reduced early clearance of Pseudomonas aeruginosa from the respiratory tract.
Volume: 166
Issue: 12
Pages: 7410-8
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7515571 | J:18444
First Author: Grubb BR
Year: 1994
Journal: Am J Physiol
Title: Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.
Volume: 266
Issue: 5 Pt 1
Pages: C1478-83
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11034402 | J:137901
First Author: Chroneos ZC
Year: 2000
Journal: J Immunol
Title: Role of cystic fibrosis transmembrane conductance regulator in pulmonary clearance of Pseudomonas aeruginosa in vivo.
Volume: 165
Issue: 7
Pages: 3941-50
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29326073 | J:261853
First Author: Li X
Year: 2018
Journal: Biochim Biophys Acta
Title: Retinoic acid promotes stem cell differentiation and embryonic development by transcriptionally activating CFTR.
Volume: 1865
Issue: 4
Pages: 605-615
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Publication
23734196 | J:202119
First Author: Huaux F
Year: 2013
Journal: PLoS One
Title: Dysregulated proinflammatory and fibrogenic phenotype of fibroblasts in cystic fibrosis.
Volume: 8
Issue: 5
Pages: e64341
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17015704 | J:139448
First Author: Allard JB
Year: 2006
Journal: J Immunol
Title: Aspergillus fumigatus generates an enhanced Th2-biased immune response in mice with defective cystic fibrosis transmembrane conductance regulator.
Volume: 177
Issue: 8
Pages: 5186-94
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19726884 | J:152692
First Author: Garcia MA
Year: 2009
Journal: J Clin Invest
Title: Normal mouse intestinal mucus release requires cystic fibrosis transmembrane regulator-dependent bicarbonate secretion.
Volume: 119
Issue: 9
Pages: 2613-22
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12578988 | J:107417
First Author: Coleman FT
Year: 2003
Journal: Proc Natl Acad Sci U S A
Title: Hypersusceptibility of cystic fibrosis mice to chronic Pseudomonas aeruginosa oropharyngeal colonization and lung infection.
Volume: 100
Issue: 4
Pages: 1949-54
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Publication
17178714 | J:120932
First Author: Sidani SM
Year: 2007
Journal: J Biol Chem
Title: DeltaF508 mutation results in impaired gastric acid secretion.
Volume: 282
Issue: 9
Pages: 6068-74
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Publication
23749967 | J:232005
First Author: Aeffner F
Year: 2013
Journal: J Infect Dis
Title: Heterozygosity for the F508del mutation in the cystic fibrosis transmembrane conductance regulator anion channel attenuates influenza severity.
Volume: 208
Issue: 5
Pages: 780-9
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31922900 | J:305408
First Author: Kramer EL
Year: 2020
Journal: Am J Respir Cell Mol Biol
Title: Subacute TGFβ Exposure Drives Airway Hyperresponsiveness in Cystic Fibrosis Mice through the PI3K Pathway.
Volume: 62
Issue: 5
Pages: 657-667
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24801204 | J:216090
First Author: Peotta VA
Year: 2014
Journal: PLoS One
Title: Reduced blood pressure of CFTR-F508del carriers correlates with diminished arterial reactivity rather than circulating blood volume in mice.
Volume: 9
Issue: 5
Pages: e96756
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35031577 | J:323270
First Author: Fan Z
Year: 2022
Journal: J Immunol
Title: Bone Marrow Transplantation Rescues Monocyte Recruitment Defect and Improves Cystic Fibrosis in Mice.
Volume: 208
Issue: 3
Pages: 745-752
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10348821 | J:55783
First Author: Steagall WK
Year: 1999
Journal: Gastroenterology
Title: Stimulation of cystic fibrosis transmembrane conductance regulator-dependent short-circuit currents across DeltaF508 murine intestines.
Volume: 116
Issue: 6
Pages: 1379-88
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15480994 | J:93426
First Author: Hirokawa M
Year: 2004
Journal: Gastroenterology
Title: Cystic fibrosis gene mutation reduces epithelial cell acidification and injury in acid-perfused mouse duodenum.
Volume: 127
Issue: 4
Pages: 1162-73
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16195538 | J:120193
First Author: Liu X
Year: 2006
Journal: Am J Respir Cell Mol Biol
Title: Species-specific differences in mouse and human airway epithelial biology of recombinant adeno-associated virus transduction.
Volume: 34
Issue: 1
Pages: 56-64
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22679004 | J:191611
First Author: Bederman I
Year: 2012
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Altered de novo lipogenesis contributes to low adipose stores in cystic fibrosis mice.
Volume: 303
Issue: 4
Pages: G507-18
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21135815 | J:170421
First Author: Hashimoto Y
Year: 2011
Journal: Lab Invest
Title: CFTR-deficiency renders mice highly susceptible to cutaneous symptoms during mite infestation.
Volume: 91
Issue: 4
Pages: 509-18
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7556083 | J:28979
First Author: van Doorninck JH
Year: 1995
Journal: EMBO J
Title: A mouse model for the cystic fibrosis delta F508 mutation.
Volume: 14
Issue: 18
Pages: 4403-11
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22833409 | J:323168
First Author: Figueiras-Fierro D
Year: 2013
Journal: J Cell Physiol
Title: Electrophysiological evidence for the presence of cystic fibrosis transmembrane conductance regulator (CFTR) in mouse sperm.
Volume: 228
Issue: 3
Pages: 590-601
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Publication
24529904 | J:208037
First Author: Le Henaff C
Year: 2014
Journal: Am J Pathol
Title: Enhanced F508del-CFTR channel activity ameliorates bone pathology in murine cystic fibrosis.
Volume: 184
Issue: 4
Pages: 1132-41
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Publication
26092868 | J:225510
First Author: Dhooghe B
Year: 2015
Journal: Biol Open
Title: Resveratrol increases F508del-CFTR dependent salivary secretion in cystic fibrosis mice.
Volume: 4
Issue: 7
Pages: 929-36
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Publication
22449949 | J:183548
First Author: Le Henaff C
Year: 2012
Journal: Am J Pathol
Title: The F508del mutation in cystic fibrosis transmembrane conductance regulator gene impacts bone formation.
Volume: 180
Issue: 5
Pages: 2068-75
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Publication
26283735 | J:233981
First Author: Fontés G
Year: 2015
Journal: Diabetes
Title: The ΔF508 Mutation in the Cystic Fibrosis Transmembrane Conductance Regulator Is Associated With Progressive Insulin Resistance and Decreased Functional β-Cell Mass in Mice.
Volume: 64
Issue: 12
Pages: 4112-22
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26060255 | J:223758
First Author: Le Henaff C
Year: 2015
Journal: J Biol Chem
Title: Increased NF-κB Activity and Decreased Wnt/β-Catenin Signaling Mediate Reduced Osteoblast Differentiation and Function in ΔF508 Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) Mice.
Volume: 290
Issue: 29
Pages: 18009-17
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11823443 | J:74740
First Author: Dickinson P
Year: 2002
Journal: Hum Mol Genet
Title: The severe G480C cystic fibrosis mutation, when replicated in the mouse, demonstrates mistrafficking, normal survival and organ-specific bioelectrics.
Volume: 11
Issue: 3
Pages: 243-51
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14529837 | J:101822
First Author: Ostrowski LE
Year: 2003
Journal: Mol Ther
Title: Targeting expression of a transgene to the airway surface epithelium using a ciliated cell-specific promoter.
Volume: 8
Issue: 4
Pages: 637-45
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Publication
19878303 | J:200383
First Author: Scott-Ward TS
Year: 2009
Journal: FEBS J
Title: Deletion of Phe508 in the first nucleotide-binding domain of the cystic fibrosis transmembrane conductance regulator increases its affinity for the heat shock cognate 70 chaperone.
Volume: 276
Issue: 23
Pages: 7097-109
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Publication
8918588 | J:37365
First Author: Moss RB
Year: 1996
Journal: Clin Exp Immunol
Title: Reduced IL-10 secretion by CD4+ T lymphocytes expressing mutant cystic fibrosis transmembrane conductance regulator (CFTR).
Volume: 106
Issue: 2
Pages: 374-88
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