| Type |
Details |
Score |
| Publication |
| First Author: |
Mimoto T |
| Year: |
2012 |
| Journal: |
Brain Res |
| Title: |
Expression of heat shock transcription factor 1 and its downstream target protein T-cell death associated gene 51 in the spinal cord of a mouse model of amyotrophic lateral sclerosis. |
| Volume: |
1488 |
|
| Pages: |
123-31 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Kim SM |
| Year: |
2011 |
| Journal: |
PLoS One |
| Title: |
Amyotrophic lateral sclerosis is associated with hypolipidemia at the presymptomatic stage in mice. |
| Volume: |
6 |
| Issue: |
3 |
| Pages: |
e17985 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Ari C |
| Year: |
2014 |
| Journal: |
PLoS One |
| Title: |
Metabolic therapy with Deanna Protocol supplementation delays disease progression and extends survival in amyotrophic lateral sclerosis (ALS) mouse model. |
| Volume: |
9 |
| Issue: |
7 |
| Pages: |
e103526 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Mishra V |
| Year: |
2020 |
| Journal: |
Nat Commun |
| Title: |
Systematic elucidation of neuron-astrocyte interaction in models of amyotrophic lateral sclerosis using multi-modal integrated bioinformatics workflow. |
| Volume: |
11 |
| Issue: |
1 |
| Pages: |
5579 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Gross SK |
| Year: |
2020 |
| Journal: |
Exp Neurol |
| Title: |
Focal and dose-dependent neuroprotection in ALS mice following AAV2-neurturin delivery. |
| Volume: |
323 |
|
| Pages: |
113091 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Audet JN |
| Year: |
2012 |
| Journal: |
PLoS One |
| Title: |
Ablation of proliferating cells in the CNS exacerbates motor neuron disease caused by mutant superoxide dismutase. |
| Volume: |
7 |
| Issue: |
4 |
| Pages: |
e34932 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Barbosa M |
| Year: |
2021 |
| Journal: |
Front Cell Dev Biol |
| Title: |
Recovery of Depleted miR-146a in ALS Cortical Astrocytes Reverts Cell Aberrancies and Prevents Paracrine Pathogenicity on Microglia and Motor Neurons. |
| Volume: |
9 |
|
| Pages: |
634355 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Crosio C |
| Year: |
2006 |
| Journal: |
Cell Death Differ |
| Title: |
Bcl2a1 serves as a switch in death of motor neurons in amyotrophic lateral sclerosis. |
| Volume: |
13 |
| Issue: |
12 |
| Pages: |
2150-3 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Wang J |
| Year: |
2021 |
| Journal: |
Mol Brain |
| Title: |
Bisperoxovanadium promotes motor neuron survival and neuromuscular innervation in amyotrophic lateral sclerosis. |
| Volume: |
14 |
| Issue: |
1 |
| Pages: |
155 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Gerovska D |
| Year: |
2023 |
| Journal: |
Cell Biosci |
| Title: |
A distinct circular DNA profile intersects with proteome changes in the genotoxic stress-related hSOD1(G93A) model of ALS. |
| Volume: |
13 |
| Issue: |
1 |
| Pages: |
170 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Perez-Gonzalez AP |
| Year: |
2022 |
| Journal: |
Glia |
| Title: |
Functional adaptation of glial cells at neuromuscular junctions in response to injury. |
| Volume: |
70 |
| Issue: |
9 |
| Pages: |
1605-1629 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Canzonetta C |
| Year: |
2008 |
| Journal: |
Am J Hum Genet |
| Title: |
DYRK1A-dosage imbalance perturbs NRSF/REST levels, deregulating pluripotency and embryonic stem cell fate in Down syndrome. |
| Volume: |
83 |
| Issue: |
3 |
| Pages: |
388-400 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Carmichael CL |
| Year: |
2009 |
| Journal: |
Blood |
| Title: |
Hematopoietic defects in the Ts1Cje mouse model of Down syndrome. |
| Volume: |
113 |
| Issue: |
9 |
| Pages: |
1929-37 |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
mutant stock, transgenic |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
mutant stock, transgenic |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
mutant stock, transgenic |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
congenic, mutant strain, transgenic |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Lhx1/Lhx1<+> Ssbp3/Ssbp3<+> |
| Background: |
involves: 129S7/SvEvBrd * C3H/He * C57BL/6 * ICR |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Ldb1/Ldb1<+> Ssbp3/Ssbp3<+> |
| Background: |
involves: C3H/He * C57BL/6 |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(Sod1*G86R)M1Jwg/? |
| Background: |
involves: C57BL/6 * FVB/N |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: C57BL/6 * SJL |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(APPV717I)1130Kha/? Tg(SOD1)76Dpr/? |
| Background: |
involves: C3H/HeJ * C57BL/6J * FVB/N |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? Tg(THY1-SNCA)1Sud/? |
| Background: |
involves: 129S6/SvEvTac * C57BL/6 * SJL |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1)2Gur/? Tg(Thy1-SOD1*G93A)T3Hgrd/? |
| Background: |
involves: C57BL/6 * CBA * FVB * SJL |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Spi1/Spi1 Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: 129S2/SvPas * C57BL/6 * SJL |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Gt(ROSA)26Sor/? Lhx3/Lhx3<+> Tg(tetO-SOD1,-luc)1Roos/? |
| Background: |
involves: 129P2/OlaHsd * 129S1/Sv * C57BL/6 |
| Zygosity: |
cn |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: C57BL/6 * CD-1 * SJL |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: C57BL/6Ico |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: C57BL/6J * C57BL/Ola * SJL/J |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: ABH * C57BL/6 * SJL |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(NEFH)200Jpj/? Tg(SOD1*G37R)29Dpr/? |
| Background: |
involves: C3H/HeJ * C57BL/6 * C57BL/6J |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(NEFH)398Jpj/? Tg(SOD1*G37R)29Dpr/? |
| Background: |
involves: C3H/HeJ * C57BL/6 * C57BL/6J |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(Prnp-CCS)17Jlel/? Tg(SOD1*G93A)1Gur/? |
| Background: |
involves: C57BL/6 * SJL |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(Prnp-Immt/SOD1*G93A)7Gmnf/? |
| Background: |
involves: C57BL/6 * CBA * SJL |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(Prnp-Immt/SOD1)1Gmnf/? |
| Background: |
involves: C57BL/6 * CBA * SJL |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Cbr1/Cbr1<+> Ts(16C-tel)1Cje/? |
| Background: |
involves: C57BL/6J * FVB/N |
| Zygosity: |
cx |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Genotype |
| Symbol: |
Tg(SOD1*G93A)1Gur/? |
| Background: |
SJL.Cg-Tg(SOD1*G93A)1Gur |
| Zygosity: |
ot |
| Has Mutant Allele: |
true |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Puttaparthi K |
| Year: |
2007 |
| Journal: |
Exp Neurol |
| Title: |
Assessing the role of immuno-proteasomes in a mouse model of familial ALS. |
| Volume: |
206 |
| Issue: |
1 |
| Pages: |
53-8 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Kang SJ |
| Year: |
2003 |
| Journal: |
J Neurosci |
| Title: |
Dissociation between neurodegeneration and caspase-11-mediated activation of caspase-1 and caspase-3 in a mouse model of amyotrophic lateral sclerosis. |
| Volume: |
23 |
| Issue: |
13 |
| Pages: |
5455-60 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Inoue H |
| Year: |
2003 |
| Journal: |
EMBO J |
| Title: |
The crucial role of caspase-9 in the disease progression of a transgenic ALS mouse model. |
| Volume: |
22 |
| Issue: |
24 |
| Pages: |
6665-74 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Celsi F |
| Year: |
2007 |
| Journal: |
Neurobiol Dis |
| Title: |
Beta-amyloid causes downregulation of calcineurin in neurons through induction of oxidative stress. |
| Volume: |
26 |
| Issue: |
2 |
| Pages: |
342-52 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Jung C |
| Year: |
2001 |
| Journal: |
Neurosci Lett |
| Title: |
Synthetic superoxide dismutase/catalase mimetics reduce oxidative stress and prolong survival in a mouse amyotrophic lateral sclerosis model. |
| Volume: |
304 |
| Issue: |
3 |
| Pages: |
157-60 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Tokuda E |
| Year: |
2008 |
| Journal: |
Exp Neurol |
| Title: |
Ammonium tetrathiomolybdate delays onset, prolongs survival, and slows progression of disease in a mouse model for amyotrophic lateral sclerosis. |
| Volume: |
213 |
| Issue: |
1 |
| Pages: |
122-8 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Feinberg K |
| Year: |
2017 |
| Journal: |
J Cell Biol |
| Title: |
A neuroprotective agent that inactivates prodegenerative TrkA and preserves mitochondria. |
| Volume: |
216 |
| Issue: |
11 |
| Pages: |
3655-3675 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Jang JY |
| Year: |
2018 |
| Journal: |
Biochim Biophys Acta Gen Subj |
| Title: |
NABi, a novel β-sheet breaker, inhibits Aβ aggregation and neuronal toxicity: Therapeutic implications for Alzheimer's disease. |
| Volume: |
1862 |
| Issue: |
1 |
| Pages: |
71-80 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Garone MG |
| Year: |
2021 |
| Journal: |
Commun Biol |
| Title: |
ALS-related FUS mutations alter axon growth in motoneurons and affect HuD/ELAVL4 and FMRP activity. |
| Volume: |
4 |
| Issue: |
1 |
| Pages: |
1025 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Suzuki N |
| Year: |
2010 |
| Journal: |
J Neurol Sci |
| Title: |
Neuronal NOS is dislocated during muscle atrophy in amyotrophic lateral sclerosis. |
| Volume: |
294 |
| Issue: |
1-2 |
| Pages: |
95-101 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Adil MS |
| Year: |
2022 |
| Journal: |
Cells |
| Title: |
Claudin-17 Deficiency in Mice Results in Kidney Injury Due to Electrolyte Imbalance and Oxidative Stress. |
| Volume: |
11 |
| Issue: |
11 |
|
|
•
•
•
•
•
|
| Publication |
| First Author: |
Maccarone P |
| Year: |
1992 |
| Journal: |
Genomics |
| Title: |
The evolution of human chromosome 21: evidence from in situ hybridization in marsupials and a monotreme. |
| Volume: |
13 |
| Issue: |
4 |
| Pages: |
1119-24 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Julien JP |
| Year: |
2006 |
| Journal: |
Biochim Biophys Acta |
| Title: |
Transgenic mouse models of amyotrophic lateral sclerosis. |
| Volume: |
1762 |
| Issue: |
11-12 |
| Pages: |
1013-24 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Lalonde R |
| Year: |
2005 |
| Journal: |
Brain Res Bull |
| Title: |
Exploratory activity and motor coordination in wild-type SOD1/SOD1 transgenic mice. |
| Volume: |
66 |
| Issue: |
2 |
| Pages: |
155-62 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Zhu X |
| Year: |
2008 |
| Journal: |
Arch Biochem Biophys |
| Title: |
Acetyl-L-carnitine suppresses apoptosis of thioredoxin 2-deficient DT40 cells. |
| Volume: |
478 |
| Issue: |
2 |
| Pages: |
154-60 |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
274
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
251
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
251
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
251
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
267
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
228
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
274
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
251
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Protein |
| Organism: |
Mus musculus/domesticus |
| Length: |
251
 |
| Fragment?: |
false |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Schininà ME |
| Year: |
1989 |
| Journal: |
Arch Biochem Biophys |
| Title: |
Primary structure from amino acid and cDNA sequences of two Cu,Zn superoxide dismutase variants from Xenopus laevis. |
| Volume: |
272 |
| Issue: |
2 |
| Pages: |
507-15 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Schininà ME |
| Year: |
1985 |
| Journal: |
FEBS Lett |
| Title: |
Primary structure of porcine Cu,Zn superoxide dismutase. |
| Volume: |
186 |
| Issue: |
2 |
| Pages: |
267-70 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Van Camp W |
| Year: |
1990 |
| Journal: |
Proc Natl Acad Sci U S A |
| Title: |
Characterization of iron superoxide dismutase cDNAs from plants obtained by genetic complementation in Escherichia coli. |
| Volume: |
87 |
| Issue: |
24 |
| Pages: |
9903-7 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Parge HE |
| Year: |
1992 |
| Journal: |
Proc Natl Acad Sci U S A |
| Title: |
Atomic structures of wild-type and thermostable mutant recombinant human Cu,Zn superoxide dismutase. |
| Volume: |
89 |
| Issue: |
13 |
| Pages: |
6109-13 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Lauranzano E |
| Year: |
2015 |
| Journal: |
Brain |
| Title: |
Peptidylprolyl isomerase A governs TARDBP function and assembly in heterogeneous nuclear ribonucleoprotein complexes. |
| Volume: |
138 |
| Issue: |
Pt 4 |
| Pages: |
974-91 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Kimura T |
| Year: |
2003 |
| Journal: |
Neurosci Lett |
| Title: |
Expression and distribution of a small-conductance calcium-activated potassium channel (SK3) protein in skeletal muscles from myotonic muscular dystrophy patients and congenital myotonic mice. |
| Volume: |
347 |
| Issue: |
3 |
| Pages: |
191-5 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Staats KA |
| Year: |
2015 |
| Journal: |
Neuroscience |
| Title: |
C-kit is important for SOD1(G93A) mouse survival independent of mast cells. |
| Volume: |
301 |
|
| Pages: |
415-20 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Li J |
| Year: |
2015 |
| Journal: |
Muscle Nerve |
| Title: |
Distinguishing neuromuscular disorders based on the passive electrical material properties of muscle. |
| Volume: |
51 |
| Issue: |
1 |
| Pages: |
49-55 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Petri S |
| Year: |
2006 |
| Journal: |
J Neurol Sci |
| Title: |
Loss of Fas ligand-function improves survival in G93A-transgenic ALS mice. |
| Volume: |
251 |
| Issue: |
1-2 |
| Pages: |
44-9 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Frey D |
| Year: |
2000 |
| Journal: |
J Neurosci |
| Title: |
Early and selective loss of neuromuscular synapse subtypes with low sprouting competence in motoneuron diseases. |
| Volume: |
20 |
| Issue: |
7 |
| Pages: |
2534-42 |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
congenic, mutant strain, transgenic, targeted mutation |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Marden JJ |
| Year: |
2007 |
| Journal: |
J Clin Invest |
| Title: |
Redox modifier genes in amyotrophic lateral sclerosis in mice. |
| Volume: |
117 |
| Issue: |
10 |
| Pages: |
2913-9 |
|
•
•
•
•
•
|
| Strain |
| Attribute String: |
congenic, mutant strain, transgenic, targeted mutation |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Van Damme P |
| Year: |
2005 |
| Journal: |
J Neuropathol Exp Neurol |
| Title: |
GluR2 deficiency accelerates motor neuron degeneration in a mouse model of amyotrophic lateral sclerosis. |
| Volume: |
64 |
| Issue: |
7 |
| Pages: |
605-12 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Bonifacino T |
| Year: |
2017 |
| Journal: |
Neuropharmacology |
| Title: |
In-vivo effects of knocking-down metabotropic glutamate receptor 5 in the SOD1G93A mouse model of amyotrophic lateral sclerosis. |
| Volume: |
123 |
|
| Pages: |
433-445 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Torazza C |
| Year: |
2023 |
| Journal: |
Cells |
| Title: |
Genetic Downregulation of the Metabotropic Glutamate Receptor Type 5 Dampens the Reactive and Neurotoxic Phenotype of Adult ALS Astrocytes. |
| Volume: |
12 |
| Issue: |
15 |
|
|
•
•
•
•
•
|
| Publication |
| First Author: |
Fischer LR |
| Year: |
2005 |
| Journal: |
Neurobiol Dis |
| Title: |
The WldS gene modestly prolongs survival in the SOD1G93A fALS mouse. |
| Volume: |
19 |
| Issue: |
1-2 |
| Pages: |
293-300 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Brambilla L |
| Year: |
2016 |
| Journal: |
Hum Mol Genet |
| Title: |
Disruption of the astrocytic TNFR1-GDNF axis accelerates motor neuron degeneration and disease progression in amyotrophic lateral sclerosis. |
| Volume: |
25 |
| Issue: |
14 |
| Pages: |
3080-3095 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Ain Q |
| Year: |
2022 |
| Journal: |
Int J Mol Sci |
| Title: |
Optimized Protocol for Proportionate CNS Cell Retrieval as a Versatile Platform for Cellular and Molecular Phenomapping in Aging and Neurodegeneration. |
| Volume: |
23 |
| Issue: |
6 |
|
|
•
•
•
•
•
|
| Publication |
| First Author: |
Harlan BA |
| Year: |
2020 |
| Journal: |
Exp Neurol |
| Title: |
Evaluation of the NAD+ biosynthetic pathway in ALS patients and effect of modulating NAD+ levels in hSOD1-linked ALS mouse models. |
| Volume: |
327 |
|
| Pages: |
113219 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Lambrechts D |
| Year: |
2003 |
| Journal: |
Nat Genet |
| Title: |
VEGF is a modifier of amyotrophic lateral sclerosis in mice and humans and protects motoneurons against ischemic death. |
| Volume: |
34 |
| Issue: |
4 |
| Pages: |
383-94 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Ng SK |
| Year: |
2015 |
| Journal: |
Exp Neurol |
| Title: |
Suppression of adenosine 2a receptor (A2aR)-mediated adenosine signaling improves disease phenotypes in a mouse model of amyotrophic lateral sclerosis. |
| Volume: |
267 |
|
| Pages: |
115-22 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Ringer C |
| Year: |
2013 |
| Journal: |
Neurobiol Dis |
| Title: |
PACAP signaling exerts opposing effects on neuroprotection and neuroinflammation during disease progression in the SOD1(G93A) mouse model of amyotrophic lateral sclerosis. |
| Volume: |
54 |
|
| Pages: |
32-42 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Larivière RC |
| Year: |
2003 |
| Journal: |
Neurobiol Dis |
| Title: |
Peripherin is not a contributing factor to motor neuron disease in a mouse model of amyotrophic lateral sclerosis caused by mutant superoxide dismutase. |
| Volume: |
13 |
| Issue: |
2 |
| Pages: |
158-66 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Moisse K |
| Year: |
2009 |
| Journal: |
Brain Res |
| Title: |
Cytosolic TDP-43 expression following axotomy is associated with caspase 3 activation in NFL-/- mice: support for a role for TDP-43 in the physiological response to neuronal injury. |
| Volume: |
1296 |
|
| Pages: |
176-86 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Damiano M |
| Year: |
2006 |
| Journal: |
J Neurochem |
| Title: |
Neural mitochondrial Ca2+ capacity impairment precedes the onset of motor symptoms in G93A Cu/Zn-superoxide dismutase mutant mice. |
| Volume: |
96 |
| Issue: |
5 |
| Pages: |
1349-61 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Liebl MP |
| Year: |
2014 |
| Journal: |
Free Radic Biol Med |
| Title: |
Dimerization of visinin-like protein 1 is regulated by oxidative stress and calcium and is a pathological hallmark of amyotrophic lateral sclerosis. |
| Volume: |
72 |
|
| Pages: |
41-54 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Rué L |
| Year: |
2019 |
| Journal: |
Acta Neuropathol Commun |
| Title: |
Reduction of ephrin-A5 aggravates disease progression in amyotrophic lateral sclerosis. |
| Volume: |
7 |
| Issue: |
1 |
| Pages: |
114 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Jokic N |
| Year: |
2006 |
| Journal: |
EMBO Rep |
| Title: |
The neurite outgrowth inhibitor Nogo-A promotes denervation in an amyotrophic lateral sclerosis model. |
| Volume: |
7 |
| Issue: |
11 |
| Pages: |
1162-7 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Dupuis L |
| Year: |
2009 |
| Journal: |
PLoS One |
| Title: |
Muscle mitochondrial uncoupling dismantles neuromuscular junction and triggers distal degeneration of motor neurons. |
| Volume: |
4 |
| Issue: |
4 |
| Pages: |
e5390 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Dupuis L |
| Year: |
2009 |
| Journal: |
Exp Neurol |
| Title: |
Mice with a mutation in the dynein heavy chain 1 gene display sensory neuropathy but lack motor neuron disease. |
| Volume: |
215 |
| Issue: |
1 |
| Pages: |
146-52 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Rossi D |
| Year: |
2008 |
| Journal: |
Cell Death Differ |
| Title: |
Focal degeneration of astrocytes in amyotrophic lateral sclerosis. |
| Volume: |
15 |
| Issue: |
11 |
| Pages: |
1691-700 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Wootz H |
| Year: |
2006 |
| Journal: |
Neuroscience |
| Title: |
Altered distribution and levels of cathepsinD and cystatins in amyotrophic lateral sclerosis transgenic mice: possible roles in motor neuron survival. |
| Volume: |
143 |
| Issue: |
2 |
| Pages: |
419-30 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Cho KJ |
| Year: |
1999 |
| Journal: |
Neuroreport |
| Title: |
Reactive astrocytes express p53 in the spinal cord of transgenic mice expressing a human Cu/Zn SOD mutation. |
| Volume: |
10 |
| Issue: |
18 |
| Pages: |
3939-43 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Dal Canto MC |
| Year: |
1995 |
| Journal: |
Brain Res |
| Title: |
Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS). |
| Volume: |
676 |
| Issue: |
1 |
| Pages: |
25-40 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Copray JC |
| Year: |
2003 |
| Journal: |
Neuroscience |
| Title: |
Expression of the low affinity neurotrophin receptor p75 in spinal motoneurons in a transgenic mouse model for amyotrophic lateral sclerosis. |
| Volume: |
116 |
| Issue: |
3 |
| Pages: |
685-94 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Dewil M |
| Year: |
2005 |
| Journal: |
Neuroreport |
| Title: |
Role of matrix metalloproteinase-9 in a mouse model for amyotrophic lateral sclerosis. |
| Volume: |
16 |
| Issue: |
4 |
| Pages: |
321-4 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Peng J |
| Year: |
2022 |
| Journal: |
Oxid Med Cell Longev |
| Title: |
MPO/HOCl Facilitates Apoptosis and Ferroptosis in the SOD1G93A Motor Neuron of Amyotrophic Lateral Sclerosis. |
| Volume: |
2022 |
|
| Pages: |
8217663 |
|
•
•
•
•
•
|
| Publication |
| First Author: |
Lee H |
| Year: |
2021 |
| Journal: |
Nat Neurosci |
| Title: |
Multi-omic analysis of selectively vulnerable motor neuron subtypes implicates altered lipid metabolism in ALS. |
| Volume: |
24 |
| Issue: |
12 |
| Pages: |
1673-1685 |
|
•
•
•
•
•
|