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Search results 2701 to 2800 out of 3140 for Sod1

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Type Details Score
Publication
16899637 | J:136461
First Author: Zona C
Year: 2006
Journal: J Neurophysiol
Title: Voltage-dependent sodium channels in spinal cord motor neurons display rapid recovery from fast inactivation in a mouse model of amyotrophic lateral sclerosis.
Volume: 96
Issue: 6
Pages: 3314-22
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10559780 | J:59666
First Author: Levine JB
Year: 1999
Journal: Glia
Title: Astrocytes interact intimately with degenerating motor neurons in mouse amyotrophic lateral sclerosis (ALS).
Volume: 28
Issue: 3
Pages: 215-24
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Publication
36555685 | J:339756
 
First Author: Hashimoto Y
Year: 2022
Journal: Int J Mol Sci
Title: Connexin 30 Deficiency Ameliorates Disease Progression at the Early Phase in a Mouse Model of Amyotrophic Lateral Sclerosis by Suppressing Glial Inflammation.
Volume: 23
Issue: 24
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Publication
16677822 | J:111941
First Author: De Winter F
Year: 2006
Journal: Mol Cell Neurosci
Title: The expression of the chemorepellent Semaphorin 3A is selectively induced in terminal Schwann cells of a subset of neuromuscular synapses that display limited anatomical plasticity and enhanced vulnerability in motor neuron disease.
Volume: 32
Issue: 1-2
Pages: 102-17
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Publication
23969236 | J:201756
 
First Author: Staats KA
Year: 2013
Journal: Neurobiol Dis
Title: Genetic ablation of phospholipase C delta 1 increases survival in SOD1(G93A) mice.
Volume: 60
Pages: 11-7
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Publication
28103314 | J:246985
First Author: Moloney EB
Year: 2017
Journal: PLoS One
Title: Expression of a Mutant SEMA3A Protein with Diminished Signalling Capacity Does Not Alter ALS-Related Motor Decline, or Confer Changes in NMJ Plasticity after BotoxA-Induced Paralysis of Male Gastrocnemic Muscle.
Volume: 12
Issue: 1
Pages: e0170314
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Publication
16427626 | J:107901
First Author: Teuchert M
Year: 2006
Journal: Exp Neurol
Title: A dynein mutation attenuates motor neuron degeneration in SOD1(G93A) mice.
Volume: 198
Issue: 1
Pages: 271-4
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Publication
25151305 | J:230213
 
First Author: Stifanese R
Year: 2014
Journal: Arch Biochem Biophys
Title: Role of calpain-1 in the early phase of experimental ALS.
Volume: 562
Pages: 1-8
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Publication
15033338 | J:179571
First Author: Raiteri L
Year: 2004
Journal: Neuropharmacology
Title: Excessive and precocious glutamate release in a mouse model of amyotrophic lateral sclerosis.
Volume: 46
Issue: 6
Pages: 782-92
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Publication
31157617 | J:277321
   
First Author: An D
Year: 2019
Journal: Elife
Title: Stem cell-derived cranial and spinal motor neurons reveal proteostatic differences between ALS resistant and sensitive motor neurons.
Volume: 8
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Publication
36982140 | J:357452
 
First Author: Picher-Martel V
Year: 2023
Journal: Int J Mol Sci
Title: Distinct Plasma Immune Profile in ALS Implicates sTNFR-II in pAMPK/Leptin Homeostasis.
Volume: 24
Issue: 6
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Publication
20832409 | J:165265
First Author: Carunchio I
Year: 2010
Journal: Exp Neurol
Title: Increased levels of p70S6 phosphorylation in the G93A mouse model of Amyotrophic Lateral Sclerosis and in valine-exposed cortical neurons in culture.
Volume: 226
Issue: 1
Pages: 218-30
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Publication
39255062 | J:357526
First Author: Germeys C
Year: 2024
Journal: Cell Rep
Title: Targeting EGLN2/PHD1 protects motor neurons and normalizes the astrocytic interferon response.
Volume: 43
Issue: 9
Pages: 114719
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Publication
30233312 | J:312559
 
First Author: Gershoni-Emek N
Year: 2018
Journal: Front Mol Neurosci
Title: Localization of RNAi Machinery to Axonal Branch Points and Growth Cones Is Facilitated by Mitochondria and Is Disrupted in ALS.
Volume: 11
Pages: 311
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Publication
38065418 | J:357507
 
First Author: Yuan Y
Year: 2024
Journal: Neurotoxicology
Title: Preferential potentiation of AMPA-mediated currents in brainstem hypoglossal motoneurons by subchronic exposure of mice expressing the human superoxide dismutase 1 G93A gene mutation to neurotoxicant methylmercury in vivo.
Volume: 100
Pages: 72-84
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Publication
24936617 | J:286070
First Author: Terashima T
Year: 2014
Journal: J Neurosci Res
Title: Stem cell factor-activated bone marrow ameliorates amyotrophic lateral sclerosis by promoting protective microglial migration.
Volume: 92
Issue: 7
Pages: 856-69
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Publication
30010873 | J:266573
First Author: Peters OM
Year: 2018
Journal: Hum Mol Genet
Title: Loss of Sarm1 does not suppress motor neuron degeneration in the SOD1G93A mouse model of amyotrophic lateral sclerosis.
Volume: 27
Issue: 21
Pages: 3761-3771
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15634228 | J:128568
First Author: Gilchrist CA
Year: 2005
Journal: Neuropathol Appl Neurobiol
Title: Effect of ubiquitin expression on neuropathogenesis in a mouse model of familial amyotrophic lateral sclerosis.
Volume: 31
Issue: 1
Pages: 20-33
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31158439 | J:282904
 
First Author: Van Acker ZP
Year: 2019
Journal: Neuroscience
Title: Non-Methylation-Linked Mechanism of REST-Induced Neuroglobin Expression Impacts Mitochondrial Phenotypes in a Mouse Model of Amyotrophic Lateral Sclerosis.
Volume: 412
Pages: 233-247
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Publication
35550203 | J:357611
First Author: Westerhaus A
Year: 2022
Journal: Acta Neuropathol Commun
Title: The distribution and function of GDE2, a regulator of spinal motor neuron survival, are disrupted in Amyotrophic Lateral Sclerosis.
Volume: 10
Issue: 1
Pages: 73
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Publication
37339001 | J:357623
 
First Author: Song J
Year: 2023
Journal: JCI Insight
Title: SRF deletion results in earlier disease onset in a mouse model of amyotrophic lateral sclerosis.
Volume: 8
Issue: 15
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34145375 | J:322021
First Author: Chen L
Year: 2021
Journal: Sci Rep
Title: Overexpression of ferroptosis defense enzyme Gpx4 retards motor neuron disease of SOD1G93A mice.
Volume: 11
Issue: 1
Pages: 12890
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Publication
38849367 | J:357629
First Author: Mora S
Year: 2024
Journal: Nat Commun
Title: Stabilization of V1 interneuron-motor neuron connectivity ameliorates motor phenotype in a mouse model of ALS.
Volume: 15
Issue: 1
Pages: 4867
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39396990 | J:357638
First Author: Hazell G
Year: 2024
Journal: Skelet Muscle
Title: Exercise, disease state and sex influence the beneficial effects of Fn14-depletion on survival and muscle pathology in the SOD1(G93A) amyotrophic lateral sclerosis (ALS) mouse model.
Volume: 14
Issue: 1
Pages: 23
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Publication
26210454 | J:232518
First Author: Kim HJ
Year: 2015
Journal: Biochem Biophys Res Commun
Title: HDAC6 maintains mitochondrial connectivity under hypoxic stress by suppressing MARCH5/MITOL dependent MFN2 degradation.
Volume: 464
Issue: 4
Pages: 1235-40
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Publication
17706428 | J:134834
First Author: Guatteo E
Year: 2007
Journal: Neurobiol Dis
Title: Altered calcium homeostasis in motor neurons following AMPA receptor but not voltage-dependent calcium channels' activation in a genetic model of amyotrophic lateral sclerosis.
Volume: 28
Issue: 1
Pages: 90-100
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Publication
26799243 | J:357704
First Author: Su XW
Year: 2016
Journal: Muscle Nerve
Title: Statins accelerate disease progression and shorten survival in SOD1(G93A) mice.
Volume: 54
Issue: 2
Pages: 284-91
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Publication
30117615 | J:357660
First Author: Gatto RG
Year: 2018
Journal: NMR Biomed
Title: In vivo diffusion MRI detects early spinal cord axonal pathology in a mouse model of amyotrophic lateral sclerosis.
Volume: 31
Issue: 8
Pages: e3954
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38217607 | J:357714
First Author: Mázala DAG
Year: 2024
Journal: J Neuromuscul Dis
Title: SERCA1 Overexpression in Skeletal Muscle Attenuates Muscle Atrophy and Improves Motor Function in a Mouse Model of ALS.
Volume: 11
Issue: 2
Pages: 315-326
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Publication
31745214 | J:357710
First Author: Wang T
Year: 2020
Journal: Cell Death Differ
Title: Necroptosis is dispensable for motor neuron degeneration in a mouse model of ALS.
Volume: 27
Issue: 5
Pages: 1728-1739
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Publication
33153123 | J:305109
 
First Author: Reinoso-Sánchez JF
Year: 2020
Journal: Int J Mol Sci
Title: Emerging Role for Linear and Circular Spermine Oxidase RNAs in Skeletal Muscle Physiopathology.
Volume: 21
Issue: 21
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Publication
28128448 | J:357662
First Author: Ramírez-Jarquín UN
Year: 2017
Journal: J Cell Physiol
Title: Chronic infusion of SOD1(G93A) astrocyte-secreted factors induces spinal motoneuron degeneration and neuromuscular dysfunction in healthy rats.
Volume: 232
Issue: 10
Pages: 2610-2615
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Publication
22606355 | J:274068
First Author: Yoo YE
Year: 2012
Journal: PLoS One
Title: Dihydrotestosterone ameliorates degeneration in muscle, axons and motoneurons and improves motor function in amyotrophic lateral sclerosis model mice.
Volume: 7
Issue: 5
Pages: e37258
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28508041 | J:258173
First Author: Chiang SC
Year: 2017
Journal: Sci Adv
Title: Mitochondrial protein-linked DNA breaks perturb mitochondrial gene transcription and trigger free radical-induced DNA damage.
Volume: 3
Issue: 4
Pages: e1602506
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Publication
30128146 | J:357784
 
First Author: Gatto RG
Year: 2018
Journal: Transl Neurodegener
Title: Ultra-High Field Diffusion MRI Reveals Early Axonal Pathology in Spinal Cord of ALS mice.
Volume: 7
Pages: 20
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Publication
33614825 | J:357817
 
First Author: Eykens C
Year: 2021
Journal: Mol Ther Methods Clin Dev
Title: AAV9-mediated gene delivery of MCT1 to oligodendrocytes does not provide a therapeutic benefit in a mouse model of ALS.
Volume: 20
Pages: 508-519
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Publication
39216080 | J:357818
First Author: Mazurie Z
Year: 2024
Journal: J Physiol
Title: Acute stress differently modulates interneurons excitability and synaptic plasticity in the primary motor cortex of wild-type and SOD1(G93A) mouse model of ALS.
Volume: 602
Issue: 19
Pages: 4987-5015
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Publication
38241160 | J:357832
First Author: López-Blanch R
Year: 2024
Journal: Neurotherapeutics
Title: Nicotinamide riboside, pterostilbene and ibudilast protect motor neurons and extend survival in ALS mice.
Volume: 21
Issue: 1
Pages: e00301
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Publication
31627428 | J:357836
 
First Author: Norante RP
Year: 2019
Journal: Int J Mol Sci
Title: ALS-Associated SOD1(G93A) Decreases SERCA Pump Levels and Increases Store-Operated Ca(2+) Entry in Primary Spinal Cord Astrocytes from a Transgenic Mouse Model.
Volume: 20
Issue: 20
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Publication
29380402 | J:357869
First Author: Clark JA
Year: 2018
Journal: Neuropathol Appl Neurobiol
Title: Epothilone D accelerates disease progression in the SOD1(G93A) mouse model of amyotrophic lateral sclerosis.
Volume: 44
Issue: 6
Pages: 590-605
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Publication
38493058 | J:357871
First Author: Milani M
Year: 2024
Journal: Neurotherapeutics
Title: Neuroprotective effects of niclosamide on disease progression via inflammatory pathways modulation in SOD1-G93A and FUS-associated amyotrophic lateral sclerosis models.
Volume: 21
Issue: 3
Pages: e00346
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Publication
17389599 | J:122717
First Author: Taylor DM
Year: 2007
Journal: J Biol Chem
Title: Tryptophan 32 potentiates aggregation and cytotoxicity of a copper/zinc superoxide dismutase mutant associated with familial amyotrophic lateral sclerosis.
Volume: 282
Issue: 22
Pages: 16329-35
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Publication
34943110 | J:357843
 
First Author: López-Blanch R
Year: 2021
Journal: Antioxidants (Basel)
Title: An Intercellular Flow of Glutathione Regulated by Interleukin 6 Links Astrocytes and the Liver in the Pathophysiology of Amyotrophic Lateral Sclerosis.
Volume: 10
Issue: 12
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Publication
20650960 | J:163630
First Author: Corti S
Year: 2010
Journal: Hum Mol Genet
Title: Systemic transplantation of c-kit+ cells exerts a therapeutic effect in a model of amyotrophic lateral sclerosis.
Volume: 19
Issue: 19
Pages: 3782-96
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Publication
23825599 | J:204346
First Author: Hirano K
Year: 2013
Journal: PLoS One
Title: Ablation of keratan sulfate accelerates early phase pathogenesis of ALS.
Volume: 8
Issue: 6
Pages: e66969
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Publication
23220634 | J:194417
First Author: Yang T
Year: 2012
Journal: Sci Transl Med
Title: Overexpression of methyl-CpG binding protein 2 impairs T(H)1 responses.
Volume: 4
Issue: 163
Pages: 163ra158
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Publication
21712032 | J:357684
First Author: Yoo YE
Year: 2011
Journal: Exp Neurol
Title: Treatment with trichostatin A initiated after disease onset delays disease progression and increases survival in a mouse model of amyotrophic lateral sclerosis.
Volume: 231
Issue: 1
Pages: 147-59
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Publication
24113175 | J:357688
First Author: Huang G
Year: 2013
Journal: Cell Death Dis
Title: Death receptor 6 (DR6) antagonist antibody is neuroprotective in the mouse SOD1G93A model of amyotrophic lateral sclerosis.
Volume: 4
Issue: 10
Pages: e841
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Publication
25434487 | J:218605
 
First Author: Battaglia G
Year: 2015
Journal: Neurobiol Dis
Title: Activation of mGlu3 metabotropic glutamate receptors enhances GDNF and GLT-1 formation in the spinal cord and rescues motor neurons in the SOD-1 mouse model of amyotrophic lateral sclerosis.
Volume: 74
Pages: 126-36
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Publication
26106294 | J:309706
 
First Author: Rojas F
Year: 2015
Journal: Front Cell Neurosci
Title: Reactive oxygen species trigger motoneuron death in non-cell-autonomous models of ALS through activation of c-Abl signaling.
Volume: 9
Pages: 203
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Publication
26598648 | J:315402
First Author: Gershoni-Emek N
Year: 2016
Journal: Mol Cell Proteomics
Title: Proteomic Analysis of Dynein-Interacting Proteins in Amyotrophic Lateral Sclerosis Synaptosomes Reveals Alterations in the RNA-Binding Protein Staufen1.
Volume: 15
Issue: 2
Pages: 506-22
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Publication
26222784 | J:230919
First Author: Genç B
Year: 2015
Journal: PLoS One
Title: Visualization of Sensory Neurons and Their Projections in an Upper Motor Neuron Reporter Line.
Volume: 10
Issue: 7
Pages: e0132815
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Publication
30483078 | J:267853
 
First Author: Garbugino L
Year: 2018
Journal: Front Behav Neurosci
Title: Prolonged Voluntary Running Negatively Affects Survival and Disease Prognosis of Male SOD1G93A Low-Copy Transgenic Mice.
Volume: 12
Pages: 275
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Publication
32750380 | J:299720
 
First Author: Konsolaki E
Year: 2020
Journal: Neuroscience
Title: Genetic Inactivation of Cholinergic C Bouton Output Improves Motor Performance but not Survival in a Mouse Model of Amyotrophic Lateral Sclerosis.
Volume: 450
Pages: 71-80
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Publication
36372157 | J:334219
 
First Author: Casañas JJ
Year: 2022
Journal: Mol Cell Neurosci
Title: Proteomic characterization of spinal cord synaptoneurosomes from Tg-SOD1/G93A mice supports a role for MNK1 and local translation in the early stages of amyotrophic lateral sclerosis.
Volume: 123
Pages: 103792
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Publication
25596588 | J:241049
First Author: Saba L
Year: 2016
Journal: Cereb Cortex
Title: Altered Functionality, Morphology, and Vesicular Glutamate Transporter Expression of Cortical Motor Neurons from a Presymptomatic Mouse Model of Amyotrophic Lateral Sclerosis.
Volume: 26
Issue: 4
Pages: 1512-28
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Publication
24498180 | J:212675
First Author: Tanaka K
Year: 2014
Journal: PLoS One
Title: A novel acylaminoimidazole derivative, WN1316, alleviates disease progression via suppression of glial inflammation in ALS mouse model.
Volume: 9
Issue: 1
Pages: e87728
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Publication
32973137 | J:296210
First Author: Trabjerg MS
Year: 2020
Journal: Sci Rep
Title: Dysregulation of metabolic pathways by carnitine palmitoyl-transferase 1 plays a key role in central nervous system disorders: experimental evidence based on animal models.
Volume: 10
Issue: 1
Pages: 15583
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Publication
18945894 | J:143558
First Author: van Zundert B
Year: 2008
Journal: J Neurosci
Title: Neonatal neuronal circuitry shows hyperexcitable disturbance in a mouse model of the adult-onset neurodegenerative disease amyotrophic lateral sclerosis.
Volume: 28
Issue: 43
Pages: 10864-74
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Publication
26362733 | J:227007
First Author: Foyez T
Year: 2015
Journal: Am J Pathol
Title: Microglial keratan sulfate epitope elicits in central nervous tissues of transgenic model mice and patients with amyotrophic lateral sclerosis.
Volume: 185
Issue: 11
Pages: 3053-65
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Publication
30713114 | J:278652
 
First Author: Pigna E
Year: 2019
Journal: EBioMedicine
Title: Histone deacetylase 4 protects from denervation and skeletal muscle atrophy in a murine model of amyotrophic lateral sclerosis.
Volume: 40
Pages: 717-732
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Publication
32038174 | J:314870
 
First Author: Gatius A
Year: 2019
Journal: Front Cell Neurosci
Title: The Y172 Monoclonal Antibody Against p-c-Jun (Ser63) Is a Marker of the Postsynaptic Compartment of C-Type Cholinergic Afferent Synapses on Motoneurons.
Volume: 13
Pages: 582
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Publication
29580378 | J:269346
   
First Author: Martínez-Silva ML
Year: 2018
Journal: Elife
Title: Hypoexcitability precedes denervation in the large fast-contracting motor units in two unrelated mouse models of ALS.
Volume: 7
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Publication
31439839 | J:279381
First Author: García-Morales V
Year: 2019
Journal: Nat Commun
Title: Sp1-regulated expression of p11 contributes to motor neuron degeneration by membrane insertion of TASK1.
Volume: 10
Issue: 1
Pages: 3784
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Publication
17868365 | J:127265
First Author: Bucher S
Year: 2007
Journal: Eur J Neurosci
Title: Vacuolization correlates with spin-spin relaxation time in motor brainstem nuclei and behavioural tests in the transgenic G93A-SOD1 mouse model of ALS.
Volume: 26
Issue: 7
Pages: 1895-901
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Publication
23711824 | J:198732
First Author: Guo Y
Year: 2013
Journal: Lab Invest
Title: The modest impact of transcription factor Nrf2 on the course of disease in an ALS animal model.
Volume: 93
Issue: 7
Pages: 825-33
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Publication
22634363 | J:192685
 
First Author: Giribaldi F
Year: 2013
Journal: Neuropharmacology
Title: Group I metabotropic glutamate autoreceptors induce abnormal glutamate exocytosis in a mouse model of amyotrophic lateral sclerosis.
Volume: 66
Pages: 253-63
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28011744 | J:239301
First Author: Pasetto L
Year: 2017
Journal: J Neurosci
Title: Targeting Extracellular Cyclophilin A Reduces Neuroinflammation and Extends Survival in a Mouse Model of Amyotrophic Lateral Sclerosis.
Volume: 37
Issue: 6
Pages: 1413-1427
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Publication
22230045 | J:184644
 
First Author: Audet JN
Year: 2012
Journal: Neuroscience
Title: Methylene blue administration fails to confer neuroprotection in two amyotrophic lateral sclerosis mouse models.
Volume: 209
Pages: 136-43
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23139902 | J:278839
First Author: Lerman BJ
Year: 2012
Journal: Brain Behav
Title: Deletion of galectin-3 exacerbates microglial activation and accelerates disease progression and demise in a SOD1(G93A) mouse model of amyotrophic lateral sclerosis.
Volume: 2
Issue: 5
Pages: 563-75
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Publication
21726643 | J:178565
First Author: Caioli S
Year: 2011
Journal: Neurobiol Dis
Title: Substance P receptor activation induces downregulation of the AMPA receptor functionality in cortical neurons from a genetic model of Amyotrophic Lateral Sclerosis.
Volume: 44
Issue: 1
Pages: 92-101
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Publication
29789581 | J:262921
First Author: Luisier R
Year: 2018
Journal: Nat Commun
Title: Intron retention and nuclear loss of SFPQ are molecular hallmarks of ALS.
Volume: 9
Issue: 1
Pages: 2010
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Publication
24803543 | J:217137
First Author: Gallart-Palau X
Year: 2014
Journal: FASEB J
Title: Neuregulin-1 is concentrated in the postsynaptic subsurface cistern of C-bouton inputs to α-motoneurons and altered during motoneuron diseases.
Volume: 28
Issue: 8
Pages: 3618-32
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Publication
35863521 | J:328355
 
First Author: Collins JM
Year: 2022
Journal: Neurobiol Dis
Title: Sarm1 knockout modifies biomarkers of neurodegeneration and spinal cord circuitry but not disease progression in the mSOD1G93A mouse model of ALS.
Volume: 172
Pages: 105821
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Publication
23145119 | J:195027
First Author: Zhao W
Year: 2012
Journal: PLoS One
Title: Caprylic triglyceride as a novel therapeutic approach to effectively improve the performance and attenuate the symptoms due to the motor neuron loss in ALS disease.
Volume: 7
Issue: 11
Pages: e49191
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Publication
26182418 | J:227425
First Author: Xie Y
Year: 2015
Journal: Neuron
Title: Endolysosomal Deficits Augment Mitochondria Pathology in Spinal Motor Neurons of Asymptomatic fALS Mice.
Volume: 87
Issue: 2
Pages: 355-70
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Publication
30017354 | J:270240
First Author: Wang L
Year: 2018
Journal: Cell Metab
Title: Mitofusin 2 Regulates Axonal Transport of Calpastatin to Prevent Neuromuscular Synaptic Elimination in Skeletal Muscles.
Volume: 28
Issue: 3
Pages: 400-414.e8
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Publication
23727509 | J:207063
 
First Author: Marconi S
Year: 2013
Journal: Neuroscience
Title: Systemic treatment with adipose-derived mesenchymal stem cells ameliorates clinical and pathological features in the amyotrophic lateral sclerosis murine model.
Volume: 248
Pages: 333-43
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Publication
34140581 | J:323699
First Author: Ohashi N
Year: 2021
Journal: Sci Rep
Title: GLT1 gene delivery based on bone marrow-derived cells ameliorates motor function and survival in a mouse model of ALS.
Volume: 11
Issue: 1
Pages: 12803
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Publication
17215390 | J:117304
First Author: Wang Y
Year: 2007
Journal: J Neurosci
Title: Vascular endothelial growth factor overexpression delays neurodegeneration and prolongs survival in amyotrophic lateral sclerosis mice.
Volume: 27
Issue: 2
Pages: 304-7
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Publication
26791230 | J:229450
First Author: Gravel M
Year: 2016
Journal: J Neurosci
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