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Search results 301 to 400 out of 1119 for Htt

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Type Details Score
Publication
27196694 | J:249069
First Author: Bayram-Weston Z
Year: 2016
Journal: PLoS One
Title: Comparison of mHTT Antibodies in Huntington's Disease Mouse Models Reveal Specific Binding Profiles and Steady-State Ubiquitin Levels with Disease Development.
Volume: 11
Issue: 5
Pages: e0155834
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Publication
23598407 | J:198508
 
First Author: Brito V
Year: 2013
Journal: Cell Death Dis
Title: Imbalance of p75(NTR)/TrkB protein expression in Huntington's disease: implication for neuroprotective therapies.
Volume: 4
Pages: e595
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Publication
25449908 | J:218769
 
First Author: Tyebji S
Year: 2015
Journal: Neurobiol Dis
Title: Hyperactivation of D1 and A2A receptors contributes to cognitive dysfunction in Huntington's disease.
Volume: 74
Pages: 41-57
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Publication
28453524 | J:247604
First Author: Coffey SR
Year: 2017
Journal: PLoS One
Title: Peripheral huntingtin silencing does not ameliorate central signs of disease in the B6.HttQ111/+ mouse model of Huntington's disease.
Volume: 12
Issue: 4
Pages: e0175968
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Publication
28171658 | J:238625
First Author: Mao Y
Year: 2016
Journal: Hum Mol Genet
Title: Targeting TEAD/YAP-transcription-dependent necrosis, TRIAD, ameliorates Huntington's disease pathology.
Volume: 25
Issue: 21
Pages: 4749-4770
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Publication
27701442 | J:251159
First Author: Yhnell E
Year: 2016
Journal: PLoS One
Title: A Longitudinal Operant Assessment of Cognitive and Behavioural Changes in the HdhQ111 Mouse Model of Huntington's Disease.
Volume: 11
Issue: 10
Pages: e0164072
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Publication
24040016 | J:207349
First Author: Saavedra A
Year: 2013
Journal: PLoS One
Title: Regulation of hippocampal cGMP levels as a candidate to treat cognitive deficits in Huntington's disease.
Volume: 8
Issue: 9
Pages: e73664
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Publication
30054496 | J:269619
First Author: Mueller KA
Year: 2018
Journal: Sci Rep
Title: Hippo Signaling Pathway Dysregulation in Human Huntington's Disease Brain and Neuronal Stem Cells.
Volume: 8
Issue: 1
Pages: 11355
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Publication
29298414 | J:271716
First Author: Virlogeux A
Year: 2018
Journal: Cell Rep
Title: Reconstituting Corticostriatal Network on-a-Chip Reveals the Contribution of the Presynaptic Compartment to Huntington's Disease.
Volume: 22
Issue: 1
Pages: 110-122
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Publication
22178857 | J:180131
First Author: Orvoen S
Year: 2012
Journal: Neurosci Lett
Title: Huntington's disease knock-in male mice show specific anxiety-like behaviour and altered neuronal maturation.
Volume: 507
Issue: 2
Pages: 127-32
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Publication
29396492 | J:262558
First Author: Minnig S
Year: 2018
Journal: Sci Rep
Title: Early Detection of Apathetic Phenotypes in Huntington's Disease Knock-in Mice Using Open Source Tools.
Volume: 8
Issue: 1
Pages: 2304
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Publication
12588797 | J:82117
First Author: Gines S
Year: 2003
Journal: Hum Mol Genet
Title: Specific progressive cAMP reduction implicates energy deficit in presymptomatic Huntington's disease knock-in mice.
Volume: 12
Issue: 5
Pages: 497-508
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Publication
21840924 | J:176675
First Author: Fossale E
Year: 2011
Journal: Hum Mol Genet
Title: Differential effects of the Huntington's disease CAG mutation in striatum and cerebellum are quantitative not qualitative.
Volume: 20
Issue: 21
Pages: 4258-67
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Publication
16687439 | J:112063
First Author: Lloret A
Year: 2006
Journal: Hum Mol Genet
Title: Genetic background modifies nuclear mutant huntingtin accumulation and HD CAG repeat instability in Huntington's disease knock-in mice.
Volume: 15
Issue: 12
Pages: 2015-24
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Publication
11494364 | J:76017
First Author: Ishiguro H
Year: 2001
Journal: J Neurosci Res
Title: Age-dependent and tissue-specific CAG repeat instability occurs in mouse knock-in for a mutant Huntington's disease gene.
Volume: 65
Issue: 4
Pages: 289-97
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Publication
28927719 | J:250587
 
First Author: Cao JK
Year: 2018
Journal: Behav Brain Res
Title: Sex-dependent behavioral impairments in the HdhQ350/+ mouse line.
Volume: 337
Pages: 34-45
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Publication
25609071 | J:220868
First Author: Jin J
Year: 2015
Journal: Hum Mol Genet
Title: Early white matter abnormalities, progressive brain pathology and motor deficits in a novel knock-in mouse model of Huntington's disease.
Volume: 24
Issue: 9
Pages: 2508-27
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Publication
11152661 | J:67074
First Author: Lin CH
Year: 2001
Journal: Hum Mol Genet
Title: Neurological abnormalities in a knock-in mouse model of Huntington's disease.
Volume: 10
Issue: 2
Pages: 137-44
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Publication
7774020 | J:25941
First Author: Nasir J
Year: 1995
Journal: Cell
Title: Targeted disruption of the Huntington's disease gene results in embryonic lethality and behavioral and morphological changes in heterozygotes.
Volume: 81
Issue: 5
Pages: 811-23
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Publication
10082833 | J:53700
First Author: O'Kusky JR
Year: 1999
Journal: Brain Res
Title: Neuronal degeneration in the basal ganglia and loss of pallido-subthalamic synapses in mice with targeted disruption of the Huntington's disease gene.
Volume: 818
Issue: 2
Pages: 468-79
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Publication
10196365 | J:54906
First Author: Shelbourne PF
Year: 1999
Journal: Hum Mol Genet
Title: A Huntington's disease CAG expansion at the murine Hdh locus is unstable and associated with behavioural abnormalities in mice.
Volume: 8
Issue: 5
Pages: 763-74
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Publication
10196373 | J:54551
First Author: Usdin MT
Year: 1999
Journal: Hum Mol Genet
Title: Impaired synaptic plasticity in mice carrying the Huntington's disease mutation.
Volume: 8
Issue: 5
Pages: 839-46
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17291464 | J:118624
 
First Author: Shelbourne P
Year: 2007
Journal: Brain Res
Title: Normal electrical properties of hippocampal neurons modelling early Huntington disease pathogenesis.
Volume: 1139
Pages: 226-34
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Publication
14570710 | J:136414
First Author: Kennedy L
Year: 2003
Journal: Hum Mol Genet
Title: Dramatic tissue-specific mutation length increases are an early molecular event in Huntington disease pathogenesis.
Volume: 12
Issue: 24
Pages: 3359-67
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Publication
10932179 | J:118556
First Author: Li H
Year: 2000
Journal: Nat Genet
Title: Amino-terminal fragments of mutant huntingtin show selective accumulation in striatal neurons and synaptic toxicity.
Volume: 25
Issue: 4
Pages: 385-9
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Publication
15781041 | J:97469
First Author: Kennedy L
Year: 2005
Journal: Brain Res
Title: Alterations in dopamine and benzodiazepine receptor binding precede overt neuronal pathology in mice modelling early Huntington disease pathogenesis.
Volume: 1039
Issue: 1-2
Pages: 14-21
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Publication
11606636 | J:72357
First Author: Li H
Year: 2001
Journal: J Neurosci
Title: Huntingtin aggregate-associated axonal degeneration is an early pathological event in Huntington's disease mice.
Volume: 21
Issue: 21
Pages: 8473-81
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Publication
11030759 | J:65412
First Author: Kennedy L
Year: 2000
Journal: Hum Mol Genet
Title: Dramatic mutation instability in HD mouse striatum: does polyglutamine load contribute to cell-specific vulnerability in Huntington's disease?
Volume: 9
Issue: 17
Pages: 2539-44
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Publication
23374344 | J:193455
First Author: Zala D
Year: 2013
Journal: Cell
Title: Vesicular glycolysis provides on-board energy for fast axonal transport.
Volume: 152
Issue: 3
Pages: 479-91
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Publication
19074039 | J:143045
First Author: Her LS
Year: 2008
Journal: J Neurosci
Title: Enhanced sensitivity of striatal neurons to axonal transport defects induced by mutant huntingtin.
Volume: 28
Issue: 50
Pages: 13662-72
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Publication
25748626 | J:224159
First Author: Mielcarek M
Year: 2015
Journal: PLoS Genet
Title: HDAC4-myogenin axis as an important marker of HD-related skeletal muscle atrophy.
Volume: 11
Issue: 3
Pages: e1005021
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Publication
17715336 | J:123681
First Author: Heng MY
Year: 2007
Journal: J Neurosci
Title: Longitudinal evaluation of the Hdh(CAG)150 knock-in murine model of Huntington's disease.
Volume: 27
Issue: 34
Pages: 8989-98
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Publication
38370446 | J:360609
First Author: Bondulich MK
Year: 2024
Journal: Brain Commun
Title: Translatable plasma and CSF biomarkers for use in mouse models of Huntington's disease.
Volume: 6
Issue: 1
Pages: fcae030
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Publication
15200234 | J:90356
First Author: Dixon KT
Year: 2004
Journal: Gene Expr
Title: Mouse Huntington's disease homolog mRNA levels: variation and allele effects.
Volume: 11
Issue: 5-6
Pages: 221-31
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Publication
20018729 | J:156460
First Author: Bradford J
Year: 2009
Journal: Proc Natl Acad Sci U S A
Title: Expression of mutant huntingtin in mouse brain astrocytes causes age-dependent neurological symptoms.
Volume: 106
Issue: 52
Pages: 22480-5
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Publication
23122961 | J:196344
First Author: Xun Z
Year: 2012
Journal: Cell Rep
Title: Targeting of XJB-5-131 to mitochondria suppresses oxidative DNA damage and motor decline in a mouse model of Huntington's disease.
Volume: 2
Issue: 5
Pages: 1137-42
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Publication
26908614 | J:233020
First Author: Polyzos A
Year: 2016
Journal: Hum Mol Genet
Title: Mitochondrial targeting of XJB-5-131 attenuates or improves pathophysiology in HdhQ150 animals with well-developed disease phenotypes.
Volume: 25
Issue: 9
Pages: 1792-802
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Publication
30930170 | J:275688
First Author: Polyzos AA
Year: 2019
Journal: Cell Metab
Title: Metabolic Reprogramming in Astrocytes Distinguishes Region-Specific Neuronal Susceptibility in Huntington Mice.
Volume: 29
Issue: 6
Pages: 1258-1273.e11
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Publication
27568644 | J:256877
First Author: Toczek M
Year: 2016
Journal: Biochim Biophys Acta
Title: An impaired metabolism of nucleotides underpins a novel mechanism of cardiac remodeling leading to Huntington's disease related cardiomyopathy.
Volume: 1862
Issue: 11
Pages: 2147-2157
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Publication
23195593 | J:196980
 
First Author: Dougherty SE
Year: 2013
Journal: Exp Neurol
Title: Purkinje cell dysfunction and loss in a knock-in mouse model of Huntington disease.
Volume: 240
Pages: 96-102
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Publication
25447230 | J:258597
 
First Author: Träger U
Year: 2015
Journal: Neurobiol Dis
Title: Characterisation of immune cell function in fragment and full-length Huntington's disease mouse models.
Volume: 73
Pages: 388-98
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Publication
30193095 | J:266738
First Author: Ast A
Year: 2018
Journal: Mol Cell
Title: mHTT Seeding Activity: A Marker of Disease Progression and Neurotoxicity in Models of Huntington's Disease.
Volume: 71
Issue: 5
Pages: 675-688.e6
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Publication
19956633 | J:155387
First Author: Moffitt H
Year: 2009
Journal: PLoS One
Title: Formation of polyglutamine inclusions in a wide range of non-CNS tissues in the HdhQ150 knock-in mouse model of Huntington's disease.
Volume: 4
Issue: 11
Pages: e8025
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Publication
19279257 | J:147069
First Author: Heng MY
Year: 2009
Journal: J Neurosci
Title: In vivo evidence for NMDA receptor-mediated excitotoxicity in a murine genetic model of Huntington disease.
Volume: 29
Issue: 10
Pages: 3200-5
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Publication
16624677 | J:112811
First Author: Brooks SP
Year: 2006
Journal: Brain Res Bull
Title: Selective extra-dimensional set shifting deficit in a knock-in mouse model of Huntington's disease.
Volume: 69
Issue: 4
Pages: 452-7
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Publication
26908599 | J:229738
First Author: Kumar A
Year: 2016
Journal: Hum Mol Genet
Title: Allelic series of Huntington's disease knock-in mice reveals expression discorrelates.
Volume: 25
Issue: 8
Pages: 1619-36
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Publication
28099507 | J:247976
First Author: Rattray I
Year: 2017
Journal: PLoS One
Title: Correlations of Behavioral Deficits with Brain Pathology Assessed through Longitudinal MRI and Histopathology in the HdhQ150/Q150 Mouse Model of Huntington's Disease.
Volume: 12
Issue: 1
Pages: e0168556
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Publication
31499139 | J:282567
 
First Author: Cao JK
Year: 2019
Journal: Neurobiol Dis
Title: Sex-dependent impaired locomotion and motor coordination in the HdhQ200/200 mouse model of Huntington's Disease.
Volume: 132
Pages: 104607
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Publication
22984513 | J:192895
First Author: Marcellin D
Year: 2012
Journal: PLoS One
Title: Fragments of HdhQ150 mutant huntingtin form a soluble oligomer pool that declines with aggregate deposition upon aging.
Volume: 7
Issue: 9
Pages: e44457
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Publication
34884469 | J:317742
 
First Author: Back MK
Year: 2021
Journal: Int J Mol Sci
Title: C57BL/6 Background Attenuates mHTT Toxicity in the Striatum of YAC128 Mice.
Volume: 22
Issue: 23
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18299573 | J:132766
First Author: Gonitel R
Year: 2008
Journal: Proc Natl Acad Sci U S A
Title: DNA instability in postmitotic neurons.
Volume: 105
Issue: 9
Pages: 3467-72
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30179155 | J:269426
   
First Author: Arnoux I
Year: 2018
Journal: Elife
Title: Metformin reverses early cortical network dysfunction and behavior changes in Huntington's disease.
Volume: 7
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Publication
34341363 | J:311426
First Author: Lovergne L
Year: 2021
Journal: Sci Rep
Title: An infrared spectral biomarker accurately predicts neurodegenerative disease class in the absence of overt symptoms.
Volume: 11
Issue: 1
Pages: 15598
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Publication
17352931 | J:128653
First Author: Woodman B
Year: 2007
Journal: Brain Res Bull
Title: The Hdh(Q150/Q150) knock-in mouse model of HD and the R6/2 exon 1 model develop comparable and widespread molecular phenotypes.
Volume: 72
Issue: 2-3
Pages: 83-97
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Publication
17394466 | J:144268
First Author: Oliveira JM
Year: 2007
Journal: J Neurochem
Title: Mitochondrial dysfunction in Huntington's disease: the bioenergetics of isolated and in situ mitochondria from transgenic mice.
Volume: 101
Issue: 1
Pages: 241-9
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Publication
24086450 | J:206483
First Author: Young D
Year: 2013
Journal: PLoS One
Title: Mutant huntingtin gene-dose impacts on aggregate deposition, DARPP32 expression and neuroinflammation in HdhQ150 mice.
Volume: 8
Issue: 9
Pages: e75108
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Publication
16237181 | J:102158
First Author: Díaz-Hernández M
Year: 2005
Journal: J Neurosci
Title: Full motor recovery despite striatal neuron loss and formation of irreversible amyloid-like inclusions in a conditional mouse model of Huntington's disease.
Volume: 25
Issue: 42
Pages: 9773-81
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10778856 | J:61490
First Author: Yamamoto A
Year: 2000
Journal: Cell
Title: Reversal of neuropathology and motor dysfunction in a conditional model of Huntington's disease.
Volume: 101
Issue: 1
Pages: 57-66
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12969257 | J:135605
First Author: Zhang Y
Year: 2003
Journal: J Neurochem
Title: Depletion of wild-type huntingtin in mouse models of neurologic diseases.
Volume: 87
Issue: 1
Pages: 101-6
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8898202 | J:36689
First Author: Mangiarini L
Year: 1996
Journal: Cell
Title: Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice.
Volume: 87
Issue: 3
Pages: 493-506
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11752065 | J:73480
First Author: Bogdanov MB
Year: 2001
Journal: J Neurochem
Title: Increased oxidative damage to DNA in a transgenic mouse model of Huntington's disease.
Volume: 79
Issue: 6
Pages: 1246-9
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11152662 | J:67073
First Author: Fain JN
Year: 2001
Journal: Hum Mol Genet
Title: Abnormalities in the functioning of adipocytes from R6/2 mice that are transgenic for the Huntington's disease mutation.
Volume: 10
Issue: 2
Pages: 145-52
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Publication
33940179 | J:322257
 
First Author: Lee M
Year: 2021
Journal: Neurobiol Dis
Title: Exosomes as a potential messenger unit during heterochronic parabiosis for amelioration of Huntington's disease.
Volume: 155
Pages: 105374
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Publication
12913073 | J:85070
First Author: Li H
Year: 2003
Journal: Hum Mol Genet
Title: Abnormal association of mutant huntingtin with synaptic vesicles inhibits glutamate release.
Volume: 12
Issue: 16
Pages: 2021-30
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Publication
11821898 | J:74541
First Author: Karpuj MV
Year: 2002
Journal: Nat Med
Title: Prolonged survival and decreased abnormal movements in transgenic model of Huntington disease, with administration of the transglutaminase inhibitor cystamine.
Volume: 8
Issue: 2
Pages: 143-9
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Publication
19124532 | J:145751
First Author: Phan J
Year: 2009
Journal: Hum Mol Genet
Title: Adipose tissue dysfunction tracks disease progression in two Huntington's disease mouse models.
Volume: 18
Issue: 6
Pages: 1006-16
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Publication
27486903 | J:256913
First Author: McCourt AC
Year: 2016
Journal: PLoS One
Title: White Adipose Tissue Browning in the R6/2 Mouse Model of Huntington's Disease.
Volume: 11
Issue: 8
Pages: e0159870
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Publication
19692612 | J:151920
First Author: Cummings DM
Year: 2009
Journal: J Neurosci
Title: Alterations in cortical excitation and inhibition in genetic mouse models of Huntington's disease.
Volume: 29
Issue: 33
Pages: 10371-86
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9267033 | J:42085
First Author: Davies SW
Year: 1997
Journal: Cell
Title: Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation.
Volume: 90
Issue: 3
Pages: 537-48
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27916455 | J:253268
First Author: Beaumont V
Year: 2016
Journal: Neuron
Title: Phosphodiesterase 10A Inhibition Improves Cortico-Basal Ganglia Function in Huntington's Disease Models.
Volume: 92
Issue: 6
Pages: 1220-1237
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Publication
11032906 | J:65206
First Author: Hickey MA
Year: 2000
Journal: J Neurochem
Title: Mice transgenic for the Huntington's disease mutation are resistant to chronic 3-nitropropionic acid-induced striatal toxicity.
Volume: 75
Issue: 5
Pages: 2163-71
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Publication
10098889 | J:53593
First Author: Reynolds GP
Year: 1999
Journal: J Neurochem
Title: Brain neurotransmitter deficits in mice transgenic for the Huntington's disease mutation.
Volume: 72
Issue: 4
Pages: 1773-6
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Publication
27646506 | J:261929
 
First Author: Ouk K
Year: 2016
Journal: Exp Neurol
Title: Progressive gene dose-dependent disruption of the methamphetamine-sensitive circadian oscillator-driven rhythms in a knock-in mouse model of Huntington's disease.
Volume: 286
Pages: 69-82
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Publication
28578004 | J:258971
 
First Author: Sebastianutto I
Year: 2017
Journal: Neurobiol Dis
Title: Alterations of striatal indirect pathway neurons precede motor deficits in two mouse models of Huntington's disease.
Volume: 105
Pages: 117-131
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Publication
30321100 | J:340213
First Author: Chanda K
Year: 2018
Journal: RNA Biol
Title: Altered Levels of Long NcRNAs Meg3 and Neat1 in Cell And Animal Models Of Huntington's Disease.
Volume: 15
Issue: 10
Pages: 1348-1363
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Publication
28031289 | J:241431
 
First Author: Ouk K
Year: 2016
Journal: Hum Mol Genet
Title: Attenuated pupillary light responses and downregulation of opsin expression parallel decline in circadian disruption in two different mouse models of Huntington's disease.
Volume: 25
Issue: 24
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Publication
10434296 | J:56820
First Author: Cha JH
Year: 1999
Journal: Philos Trans R Soc Lond B Biol Sci
Title: Altered neurotransmitter receptor expression in transgenic mouse models of Huntington's disease.
Volume: 354
Issue: 1386
Pages: 981-9
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Publication
11592850 | J:72696
First Author: Liévens JC
Year: 2001
Journal: Neurobiol Dis
Title: Impaired glutamate uptake in the R6 Huntington's disease transgenic mice.
Volume: 8
Issue: 5
Pages: 807-21
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Publication
28384474 | J:256089
First Author: Gasset-Rosa F
Year: 2017
Journal: Neuron
Title: Polyglutamine-Expanded Huntingtin Exacerbates Age-Related Disruption of Nuclear Integrity and Nucleocytoplasmic Transport.
Volume: 94
Issue: 1
Pages: 48-57.e4
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Publication
24906892 | J:218075
First Author: Marangoni M
Year: 2014
Journal: Neurobiol Aging
Title: Age-related axonal swellings precede other neuropathological hallmarks in a knock-in mouse model of Huntington's disease.
Volume: 35
Issue: 10
Pages: 2382-93
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Publication
10078572 | J:53776
First Author: Hurlbert MS
Year: 1999
Journal: Diabetes
Title: Mice transgenic for an expanded CAG repeat in the Huntington's disease gene develop diabetes.
Volume: 48
Issue: 3
Pages: 649-51
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Publication
10632104 | J:60060
First Author: Tabrizi SJ
Year: 2000
Journal: Ann Neurol
Title: Mitochondrial dysfunction and free radical damage in the Huntington R6/2 transgenic mouse.
Volume: 47
Issue: 1
Pages: 80-6
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10533044 | J:76018
First Author: Levine MS
Year: 1999
Journal: J Neurosci Res
Title: Enhanced sensitivity to N-methyl-D-aspartate receptor activation in transgenic and knockin mouse models of Huntington's disease.
Volume: 58
Issue: 4
Pages: 515-32
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Publication
33370315 | J:299485
First Author: Heikkinen T
Year: 2020
Journal: PLoS One
Title: Rapid and robust patterns of spontaneous locomotor deficits in mouse models of Huntington's disease.
Volume: 15
Issue: 12
Pages: e0243052
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Publication
34239412 | J:321258
 
First Author: Schindler F
Year: 2021
Journal: Front Neurosci
Title: Small, Seeding-Competent Huntingtin Fibrils Are Prominent Aggregate Species in Brains of zQ175 Huntington's Disease Knock-in Mice.
Volume: 15
Pages: 682172
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Publication
18504298 | J:137025
First Author: Wang CE
Year: 2008
Journal: J Cell Biol
Title: Suppression of neuropil aggregates and neurological symptoms by an intracellular antibody implicates the cytoplasmic toxicity of mutant huntingtin.
Volume: 181
Issue: 5
Pages: 803-16
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18768691 | J:141171
First Author: Walker AG
Year: 2008
Journal: J Neurosci
Title: Altered information processing in the prefrontal cortex of Huntington's disease mouse models.
Volume: 28
Issue: 36
Pages: 8973-82
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27381424 | J:236790
First Author: Dufour BD
Year: 2016
Journal: Exp Neurol
Title: Corticosterone dysregulation exacerbates disease progression in the R6/2 transgenic mouse model of Huntington's disease.
Volume: 283
Issue: Pt A
Pages: 308-17
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21505144 | J:182068
First Author: She P
Year: 2011
Journal: Am J Physiol Endocrinol Metab
Title: Molecular characterization of skeletal muscle atrophy in the R6/2 mouse model of Huntington's disease.
Volume: 301
Issue: 1
Pages: E49-61
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11880489 | J:75156
First Author: Ferrante RJ
Year: 2002
Journal: J Neurosci
Title: Therapeutic effects of coenzyme Q10 and remacemide in transgenic mouse models of Huntington's disease.
Volume: 22
Issue: 5
Pages: 1592-9
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28993428 | J:263524
First Author: Alpaugh M
Year: 2017
Journal: EMBO Mol Med
Title: Disease-modifying effects of ganglioside GM1 in Huntington's disease models.
Volume: 9
Issue: 11
Pages: 1537-1557
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30061661 | J:268385
First Author: Pido-Lopez J
Year: 2018
Journal: Sci Rep
Title: In vivo neutralization of the protagonist role of macrophages during the chronic inflammatory stage of Huntington's disease.
Volume: 8
Issue: 1
Pages: 11447
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16446101 | J:108616
First Author: Gomez GT
Year: 2006
Journal: Mol Cell Neurosci
Title: Brain-specific factors in combination with mutant huntingtin induce gene-specific transcriptional dysregulation.
Volume: 31
Issue: 4
Pages: 661-75
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11520890 | J:71210
First Author: Hansson O
Year: 2001
Journal: J Neurochem
Title: Partial resistance to malonate-induced striatal cell death in transgenic mouse models of Huntington's disease is dependent on age and CAG repeat length.
Volume: 78
Issue: 4
Pages: 694-703
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10739639 | J:61687
First Author: Menalled L
Year: 2000
Journal: Exp Neurol
Title: Decrease in striatal enkephalin mRNA in mouse models of Huntington's disease.
Volume: 162
Issue: 2
Pages: 328-42
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12223581 | J:79137
First Author: Menalled LB
Year: 2002
Journal: J Neurosci
Title: Early motor dysfunction and striosomal distribution of huntingtin microaggregates in Huntington's disease knock-in mice.
Volume: 22
Issue: 18
Pages: 8266-76
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17335925 | J:122514
First Author: Sawada H
Year: 2007
Journal: Neurosci Res
Title: Characterization of neuron-specific huntingtin aggregates in human huntingtin knock-in mice.
Volume: 57
Issue: 4
Pages: 559-73
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10448198 | J:56438
First Author: Manley K
Year: 1999
Journal: Brain Res
Title: Instability of the CAG repeat in immortalized fibroblast cell cultures from Huntington's disease transgenic mice.
Volume: 835
Issue: 1
Pages: 74-9
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30182387 | J:267306
First Author: Martínez-Ramírez C
Year: 2018
Journal: J Neurochem
Title: Altered excitability and exocytosis in chromaffin cells from the R6/1 mouse model of Huntington's disease is linked to over-expression of mutated huntingtin.
Volume: 147
Issue: 4
Pages: 454-476
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11906693 | J:75438
First Author: Zeron MM
Year: 2002
Journal: Neuron
Title: Increased sensitivity to N-methyl-D-aspartate receptor-mediated excitotoxicity in a mouse model of Huntington's disease.
Volume: 33
Issue: 6
Pages: 849-60
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