| Primary Identifier | IPR026501 | Type | Family |
| Short Name | Limbin/EVC |
| description | EVC is a protein mutated in the human chondroectodermal dysplasia Ellis-van Creveld syndrome. Limbin or EVC2 interacts with AVC []. They act as positive mediators of Hedgehog signaling and play a critical role in bone formation and skeletal development []. |