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DO Term : frontotemporal dementia [DOID:9255] Disease Ontology

Namespace  disease_ontology Obsolete  false
description  A dementia characterized by progressive neuronal loss predominantly involving the frontal and/or temporal lobes of the brain resulting in a gradual and progressive decline in behavior or language.
  • synonyms:
  • multiple system tauopathy with presenile dementia,
  • pallidopontonigral degeneration,
  • MESH:C563003,
  • frontotemporal lobar degeneration,
  • UMLS_CUI:C0520716,
  • 600274,
  • ORDO:282,
  • SNOMEDCT_US_2023_03_01:42369001,
  • OMIM:600274,
  • GARD:8436,
  • Wilhemsen-Lynch disease
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