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DO Term : vulval Paget's disease [DOID:2097] Disease Ontology

Namespace  disease_ontology Obsolete  false
description  A vulva adenocarcinoma that is characterized by distinctive large cells with prominent cytoplasm, referred to as Paget cells and is an intraepithelial neoplasm of epithelial origin expressing apocrine or eccrine glandular-like features.
  • synonyms:
  • NCI:C4027,
  • SNOMEDCT_US_2023_03_01:254898001,
  • Paget's disease of vulva,
  • vulval Paget disease,
  • UMLS_CUI:C1275217,
  • Vulvar Paget's disease
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