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Search results 201 to 300 out of 1127 for Cftr

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Type Details Score
Publication
24400140 | J:227957
First Author: Wallace HL
Year: 2013
Journal: Physiol Rep
Title: Abnormal tracheal smooth muscle function in the CF mouse.
Volume: 1
Issue: 6
Pages: e00138
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Publication
25557910 | J:323264
First Author: Bronckers AL
Year: 2015
Journal: Eur J Oral Sci
Title: Composition of mineralizing incisor enamel in cystic fibrosis transmembrane conductance regulator-deficient mice.
Volume: 123
Issue: 1
Pages: 9-16
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Publication
20004757 | J:162060
First Author: Bronckers A
Year: 2010
Journal: Bone
Title: The cystic fibrosis transmembrane conductance regulator (CFTR) is expressed in maturation stage ameloblasts, odontoblasts and bone cells.
Volume: 46
Issue: 4
Pages: 1188-96
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Publication
24251786 | J:232087
First Author: Xue X
Year: 2014
Journal: Am J Respir Cell Mol Biol
Title: Synthetic aminoglycosides efficiently suppress cystic fibrosis transmembrane conductance regulator nonsense mutations and are enhanced by ivacaftor.
Volume: 50
Issue: 4
Pages: 805-16
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Publication
36077390 | J:336689
 
First Author: Tan X
Year: 2022
Journal: Int J Mol Sci
Title: The NHE3 Inhibitor Tenapanor Prevents Intestinal Obstructions in CFTR-Deleted Mice.
Volume: 23
Issue: 17
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Publication
15528257 | J:97414
First Author: Bijvelds MJ
Year: 2005
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Fat absorption in cystic fibrosis mice is impeded by defective lipolysis and post-lipolytic events.
Volume: 288
Issue: 4
Pages: G646-53
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Publication
7714835 | J:23238
 
First Author: Cuthbert AW
Year: 1995
Journal: J Physiol
Title: The genetic advantage hypothesis in cystic fibrosis heterozygotes: a murine study.
Volume: 482 ( Pt 2)
Pages: 449-54
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Publication
7518307 | J:113056
First Author: Cuthbert AW
Year: 1994
Journal: Br J Pharmacol
Title: Chloride secretion in response to guanylin in colonic epithelial from normal and transgenic cystic fibrosis mice.
Volume: 112
Issue: 1
Pages: 31-6
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Publication
8823295 | J:35364
First Author: French PJ
Year: 1996
Journal: J Clin Invest
Title: A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo.
Volume: 98
Issue: 6
Pages: 1304-12
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Publication
12226741 | J:133060
First Author: Du M
Year: 2002
Journal: J Mol Med (Berl)
Title: Aminoglycoside suppression of a premature stop mutation in a Cftr-/- mouse carrying a human CFTR-G542X transgene.
Volume: 80
Issue: 9
Pages: 595-604
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Publication
22301109 | J:187495
First Author: Bodewes FA
Year: 2012
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Ursodeoxycholate modulates bile flow and bile salt pool independently from the cystic fibrosis transmembrane regulator (Cftr) in mice.
Volume: 302
Issue: 9
Pages: G1035-42
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Publication
9922375 | -
First Author: Sheppard DN
Year: 1999
Journal: Physiol Rev
Title: Structure and function of the CFTR chloride channel.
Volume: 79
Issue: 1 Suppl
Pages: S23-45
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Gene
111674471 | LOC111674471
Type: gene
Organism: human
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Gene
111674472 | LOC111674472
Type: gene
Organism: human
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Publication
19221439 | J:146793
First Author: Singh AK
Year: 2009
Journal: J Clin Invest
Title: Differential roles of NHERF1, NHERF2, and PDZK1 in regulating CFTR-mediated intestinal anion secretion in mice.
Volume: 119
Issue: 3
Pages: 540-50
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Publication
12692180 | J:105419
First Author: Bachmann O
Year: 2003
Journal: J Physiol
Title: Expression and regulation of the Na+-K+-2Cl- cotransporter NKCC1 in the normal and CFTR-deficient murine colon.
Volume: 549
Issue: Pt 2
Pages: 525-36
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Publication
9097955 | J:39502
First Author: Trezise AE
Year: 1997
Journal: Hum Mol Genet
Title: Co-ordinate regulation of the cystic fibrosis and multidrug resistance genes in cystic fibrosis knockout mice.
Volume: 6
Issue: 4
Pages: 527-37
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Publication
25012520 | J:276489
First Author: Jalali R
Year: 2014
Journal: Cell Tissue Res
Title: NBCe1 (SLC4A4) a potential pH regulator in enamel organ cells during enamel development in the mouse.
Volume: 358
Issue: 2
Pages: 433-42
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Publication
16888286 | J:130524
First Author: Guilbault C
Year: 2007
Journal: Am J Respir Cell Mol Biol
Title: Cystic fibrosis mouse models.
Volume: 36
Issue: 1
Pages: 1-7
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Publication
18779379 | J:146039
First Author: Zheng W
Year: 2009
Journal: FASEB J
Title: Hypoxia inducible factor-1 (HIF-1)-mediated repression of cystic fibrosis transmembrane conductance regulator (CFTR) in the intestinal epithelium.
Volume: 23
Issue: 1
Pages: 204-13
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Publication
27744011 | J:255129
 
First Author: Bronckers AL
Year: 2017
Journal: Bone
Title: Magnesium, pH regulation and modulation by mouse ameloblasts exposed to fluoride.
Volume: 94
Pages: 56-64
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Publication
22003093 | J:183328
First Author: Grubb BR
Year: 2012
Journal: Am J Physiol Lung Cell Mol Physiol
Title: Transgenic hCFTR expression fails to correct β-ENaC mouse lung disease.
Volume: 302
Issue: 2
Pages: L238-47
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Publication
30013481 | J:275628
 
First Author: Al-Ansari S
Year: 2018
Journal: Front Physiol
Title: The Importance of Connexin 43 in Enamel Development and Mineralization.
Volume: 9
Pages: 750
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Publication
31470114 | J:323259
First Author: Ikpa PT
Year: 2020
Journal: Cell Mol Gastroenterol Hepatol
Title: Impaired Intestinal Farnesoid X Receptor Signaling in Cystic Fibrosis Mice.
Volume: 9
Issue: 1
Pages: 47-60
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Publication
22802588 | J:202084
First Author: Xiao F
Year: 2012
Journal: J Physiol
Title: Rescue of epithelial HCO3- secretion in murine intestine by apical membrane expression of the cystic fibrosis transmembrane conductance regulator mutant F508del.
Volume: 590
Issue: 21
Pages: 5317-34
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Publication
27301931 | J:251366
First Author: van der Mark VA
Year: 2016
Journal: Biochim Biophys Acta
Title: The phospholipid flippase ATP8B1 mediates apical localization of the cystic fibrosis transmembrane regulator.
Volume: 1863
Issue: 9
Pages: 2280-8
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Publication
7870054 | J:23278
First Author: Navarro P
Year: 1995
Journal: Mol Immunol
Title: The complete cDNA and deduced amino acid sequence of equine IgE.
Volume: 32
Issue: 1
Pages: 1-8
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Publication
9277371 | J:42654
First Author: MacVinish LJ
Year: 1997
Journal: Am J Physiol
Title: Normalization of ion transport in murine cystic fibrosis nasal epithelium using gene transfer.
Volume: 273
Issue: 2 Pt 1
Pages: C734-40
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Publication
10678637 | J:60474
First Author: Ghosal S
Year: 2000
Journal: Eur Respir J
Title: Sodium channel blockers and uridine triphosphate: effects on nasal potential difference in cystic fibrosis mice.
Volume: 15
Issue: 1
Pages: 146-50
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Publication
1355249 | J:2584
First Author: Colledge WH
Year: 1992
Journal: Lancet
Title: Cystic fibrosis mouse with intestinal obstruction.
Volume: 340
Issue: 8820
Pages: 680
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Publication
18272502 | J:132180
First Author: Du M
Year: 2008
Journal: Proc Natl Acad Sci U S A
Title: PTC124 is an orally bioavailable compound that promotes suppression of the human CFTR-G542X nonsense allele in a CF mouse model.
Volume: 105
Issue: 6
Pages: 2064-9
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Publication
20624691 | J:306494
First Author: Braun J
Year: 2010
Journal: J Cyst Fibros
Title: Quantitative expression analyses of candidates for alternative anion conductance in cystic fibrosis mouse models.
Volume: 9
Issue: 5
Pages: 351-64
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Publication
24965066 | J:232055
First Author: Liu X
Year: 2015
Journal: Pflugers Arch
Title: Loss of Slc26a9 anion transporter alters intestinal electrolyte and HCO3(-) transport and reduces survival in CFTR-deficient mice.
Volume: 467
Issue: 6
Pages: 1261-75
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Publication
20351045 | J:176771
First Author: Sørensen MV
Year: 2010
Journal: J Physiol
Title: Adrenaline-induced colonic K+ secretion is mediated by KCa1.1 (BK) channels.
Volume: 588
Issue: Pt 10
Pages: 1763-77
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Publication
21658634 | J:230489
 
First Author: Wilke M
Year: 2011
Journal: J Cyst Fibros
Title: Mouse models of cystic fibrosis: phenotypic analysis and research applications.
Volume: 10 Suppl 2
Pages: S152-71
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Publication
26365583 | J:227718
First Author: Gibson-Corley KN
Year: 2016
Journal: J Pathol
Title: Pancreatic pathophysiology in cystic fibrosis.
Volume: 238
Issue: 2
Pages: 311-20
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Publication
19136563 | J:323250
First Author: Du M
Year: 2009
Journal: J Biol Chem
Title: Poly-L-aspartic acid enhances and prolongs gentamicin-mediated suppression of the CFTR-G542X mutation in a cystic fibrosis mouse model.
Volume: 284
Issue: 11
Pages: 6885-92
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Publication
20231275 | J:162962
First Author: Skals M
Year: 2010
Journal: J Biol Chem
Title: Escherichia coli alpha-hemolysin triggers shrinkage of erythrocytes via K(Ca)3.1 and TMEM16A channels with subsequent phosphatidylserine exposure.
Volume: 285
Issue: 20
Pages: 15557-65
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Publication
26403673 | J:306590
First Author: Bronckers AL
Year: 2015
Journal: J Dent Res
Title: Ameloblast Modulation and Transport of Cl⁻, Na⁺, and K⁺ during Amelogenesis.
Volume: 94
Issue: 12
Pages: 1740-7
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Publication
7527588 | J:21934
First Author: Zhou L
Year: 1994
Journal: Science
Title: Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR.
Volume: 266
Issue: 5191
Pages: 1705-8
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Publication
7482032 | J:29656
First Author: Hasty P
Year: 1995
Journal: Somat Cell Mol Genet
Title: Severe phenotype in mice with termination mutation in exon 2 of cystic fibrosis gene.
Volume: 21
Issue: 3
Pages: 177-87
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Publication
7524148 | J:20778
First Author: Gabriel SE
Year: 1994
Journal: Science
Title: Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model.
Volume: 266
Issue: 5182
Pages: 107-9
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Publication
1380723 | J:2079
First Author: Snouwaert JN
Year: 1992
Journal: Science
Title: An animal model for cystic fibrosis made by gene targeting.
Volume: 257
Issue: 5073
Pages: 1083-8
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Publication
7691356 | J:48374
First Author: Delaney SJ
Year: 1993
Journal: Nat Genet
Title: Cystic fibrosis transmembrane conductance regulator splice variants are not conserved and fail to produce chloride channels.
Volume: 4
Issue: 4
Pages: 426-31
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Publication
26823428 | J:240085
First Author: Shah VS
Year: 2016
Journal: Science
Title: Airway acidification initiates host defense abnormalities in cystic fibrosis mice.
Volume: 351
Issue: 6272
Pages: 503-7
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Publication
21884936 | J:176213
First Author: Gee HY
Year: 2011
Journal: Cell
Title: Rescue of ΔF508-CFTR trafficking via a GRASP-dependent unconventional secretion pathway.
Volume: 146
Issue: 5
Pages: 746-60
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Publication
16481627 | J:107307
First Author: Bruscia EM
Year: 2006
Journal: Proc Natl Acad Sci U S A
Title: Assessment of cystic fibrosis transmembrane conductance regulator (CFTR) activity in CFTR-null mice after bone marrow transplantation.
Volume: 103
Issue: 8
Pages: 2965-70
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Publication
7545494 | J:27734
First Author: Colledge WH
Year: 1995
Journal: Nat Genet
Title: Generation and characterization of a delta F508 cystic fibrosis mouse model.
Volume: 10
Issue: 4
Pages: 445-52
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Publication
8605891 | J:32766
First Author: Delaney SJ
Year: 1996
Journal: EMBO J
Title: Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype-phenotype correlations.
Volume: 15
Issue: 5
Pages: 955-63
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Publication
11978765 | J:133160
First Author: Oceandy D
Year: 2002
Journal: Hum Mol Genet
Title: Gene complementation of airway epithelium in the cystic fibrosis mouse is necessary and sufficient to correct the pathogen clearance and inflammatory abnormalities.
Volume: 11
Issue: 9
Pages: 1059-67
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Publication
24373976 | J:323177
First Author: Bazett M
Year: 2014
Journal: J Cyst Fibros
Title: Airway hyperresponsiveness in FVB/N delta F508 cystic fibrosis transmembrane conductance regulator mice.
Volume: 13
Issue: 4
Pages: 378-83
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Publication
20570219 | J:233126
First Author: Paradis J
Year: 2010
Journal: J Cyst Fibros
Title: Osteopenia in Cftr-deltaF508 mice.
Volume: 9
Issue: 4
Pages: 239-45
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Publication
23269368 | J:232013
First Author: Sellers ZM
Year: 2013
Journal: J Cyst Fibros
Title: Left ventricular and aortic dysfunction in cystic fibrosis mice.
Volume: 12
Issue: 5
Pages: 517-24
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Publication
7560099 | J:29074
First Author: Zeiher BG
Year: 1995
Journal: J Clin Invest
Title: A mouse model for the delta F508 allele of cystic fibrosis.
Volume: 96
Issue: 4
Pages: 2051-64
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Publication
20478977 | J:176765
First Author: Muchekehu RW
Year: 2010
Journal: J Physiol
Title: A new role for bicarbonate secretion in cervico-uterine mucus release.
Volume: 588
Issue: Pt 13
Pages: 2329-42
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Publication
15336594 | J:92512
First Author: Dif F
Year: 2004
Journal: Bone
Title: Severe osteopenia in CFTR-null mice.
Volume: 35
Issue: 3
Pages: 595-603
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Publication
12161463 | J:105940
First Author: Arquitt CK
Year: 2002
Journal: J Dent Res
Title: Cystic fibrosis transmembrane regulator gene (CFTR) is associated with abnormal enamel formation.
Volume: 81
Issue: 7
Pages: 492-6
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Publication
8827771 | J:35002
First Author: Kent G
Year: 1996
Journal: Pediatr Res
Title: Phenotypic abnormalities in long-term surviving cystic fibrosis mice.
Volume: 40
Issue: 2
Pages: 233-41
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Publication
17519339 | J:122297
First Author: Xu WM
Year: 2007
Journal: Proc Natl Acad Sci U S A
Title: Cystic fibrosis transmembrane conductance regulator is vital to sperm fertilizing capacity and male fertility.
Volume: 104
Issue: 23
Pages: 9816-21
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Publication
15105504 | J:90068
First Author: Egan ME
Year: 2004
Journal: Science
Title: Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects.
Volume: 304
Issue: 5670
Pages: 600-2
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Publication
27834953 | J:259869
First Author: Liu Z
Year: 2017
Journal: Cell Death Differ
Title: CFTR-β-catenin interaction regulates mouse embryonic stem cell differentiation and embryonic development.
Volume: 24
Issue: 1
Pages: 98-110
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Publication
1380724 | J:23817
First Author: Clarke LL
Year: 1992
Journal: Science
Title: Defective epithelial chloride transport in a gene-targeted mouse model of cystic fibrosis.
Volume: 257
Issue: 5073
Pages: 1125-8
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Publication
7504552 | J:15842
First Author: Alton EW
Year: 1993
Journal: Nat Genet
Title: Non-invasive liposome-mediated gene delivery can correct the ion transport defect in cystic fibrosis mutant mice.
Volume: 5
Issue: 2
Pages: 135-42
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Publication
1284640 | J:23857
First Author: Whitsett JA
Year: 1992
Journal: Nat Genet
Title: Human cystic fibrosis transmembrane conductance regulator directed to respiratory epithelial cells of transgenic mice.
Volume: 2
Issue: 1
Pages: 13-20
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Publication
9613608 | J:47599
First Author: Wang S
Year: 1998
Journal: FEBS Lett
Title: Peptide binding consensus of the NHE-RF-PDZ1 domain matches the C-terminal sequence of cystic fibrosis transmembrane conductance regulator (CFTR).
Volume: 427
Issue: 1
Pages: 103-8
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Publication
15064229 | J:102142
First Author: Kaur S
Year: 2004
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Acidic duodenal pH alters gene expression in the cystic fibrosis mouse pancreas.
Volume: 287
Issue: 2
Pages: G480-90
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Publication
7556083 | J:28979
First Author: van Doorninck JH
Year: 1995
Journal: EMBO J
Title: A mouse model for the cystic fibrosis delta F508 mutation.
Volume: 14
Issue: 18
Pages: 4403-11
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Publication
22833409 | J:323168
First Author: Figueiras-Fierro D
Year: 2013
Journal: J Cell Physiol
Title: Electrophysiological evidence for the presence of cystic fibrosis transmembrane conductance regulator (CFTR) in mouse sperm.
Volume: 228
Issue: 3
Pages: 590-601
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Publication
21135815 | J:170421
First Author: Hashimoto Y
Year: 2011
Journal: Lab Invest
Title: CFTR-deficiency renders mice highly susceptible to cutaneous symptoms during mite infestation.
Volume: 91
Issue: 4
Pages: 509-18
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Publication
23734196 | J:202119
First Author: Huaux F
Year: 2013
Journal: PLoS One
Title: Dysregulated proinflammatory and fibrogenic phenotype of fibroblasts in cystic fibrosis.
Volume: 8
Issue: 5
Pages: e64341
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Publication
25271146 | J:219840
First Author: Pfister S
Year: 2015
Journal: J Comp Neurol
Title: Novel role of cystic fibrosis transmembrane conductance regulator in maintaining adult mouse olfactory neuronal homeostasis.
Volume: 523
Issue: 3
Pages: 406-30
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Publication
17873061 | J:125319
First Author: Ostedgaard LS
Year: 2007
Journal: Proc Natl Acad Sci U S A
Title: Processing and function of CFTR-DeltaF508 are species-dependent.
Volume: 104
Issue: 39
Pages: 15370-5
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Publication
15289377 | J:102151
First Author: Chen H
Year: 2004
Journal: Circulation
Title: Targeted inactivation of cystic fibrosis transmembrane conductance regulator chloride channel gene prevents ischemic preconditioning in isolated mouse heart.
Volume: 110
Issue: 6
Pages: 700-4
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Publication
31922900 | J:305408
First Author: Kramer EL
Year: 2020
Journal: Am J Respir Cell Mol Biol
Title: Subacute TGFβ Exposure Drives Airway Hyperresponsiveness in Cystic Fibrosis Mice through the PI3K Pathway.
Volume: 62
Issue: 5
Pages: 657-667
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Publication
18790990 | J:142605
First Author: Manson ME
Year: 2008
Journal: Am J Physiol Lung Cell Mol Physiol
Title: cAMP-mediated regulation of cholesterol accumulation in cystic fibrosis and Niemann-Pick type C cells.
Volume: 295
Issue: 5
Pages: L809-19
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Publication
29423078 | J:321497
First Author: Yang X
Year: 2018
Journal: Oncotarget
Title: Molecular mechanisms of calcium signaling in the modulation of small intestinal ion transports and bicarbonate secretion.
Volume: 9
Issue: 3
Pages: 3727-3740
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Publication
16418321 | J:108346
First Author: Guilbault C
Year: 2006
Journal: Physiol Genomics
Title: Distinct pattern of lung gene expression in the Cftr-KO mice developing spontaneous lung disease compared with their littermate controls.
Volume: 25
Issue: 2
Pages: 179-93
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Publication
9124365 | J:38820
First Author: Grubb BR
Year: 1997
Journal: Am J Physiol
Title: Enhanced colonic Na+ absorption in cystic fibrosis mice versus normal mice.
Volume: 272
Issue: 2 Pt 1
Pages: G393-400
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Publication
15064232 | J:95677
First Author: Blanco PG
Year: 2004
Journal: Am J Physiol Gastrointest Liver Physiol
Title: Induction of colitis in cftr-/- mice results in bile duct injury.
Volume: 287
Issue: 2
Pages: G491-6
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Publication
18054564 | J:135618
First Author: Young FD
Year: 2007
Journal: Gastroenterology
Title: Amelioration of cystic fibrosis intestinal mucous disease in mice by restoration of mCLCA3.
Volume: 133
Issue: 6
Pages: 1928-37
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Publication
29326073 | J:261853
First Author: Li X
Year: 2018
Journal: Biochim Biophys Acta
Title: Retinoic acid promotes stem cell differentiation and embryonic development by transcriptionally activating CFTR.
Volume: 1865
Issue: 4
Pages: 605-615
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Publication
12164788 | J:79985
First Author: Thomsson KA
Year: 2002
Journal: Biochem J
Title: Intestinal mucins from cystic fibrosis mice show increased fucosylation due to an induced Fucalpha1-2 glycosyltransferase.
Volume: 367
Issue: Pt 3
Pages: 609-16
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Publication
7515571 | J:18444
First Author: Grubb BR
Year: 1994
Journal: Am J Physiol
Title: Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.
Volume: 266
Issue: 5 Pt 1
Pages: C1478-83
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Publication
14977953 | J:88586
First Author: van Heeckeren AM
Year: 2004
Journal: Infect Immun
Title: Nutritional effects on host response to lung infections with mucoid Pseudomonas aeruginosa in mice.
Volume: 72
Issue: 3
Pages: 1479-86
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Publication
12110684 | J:79311
First Author: DeCarvalho AC
Year: 2002
Journal: J Biol Chem
Title: Mutations in the nucleotide binding domain 1 signature motif region rescue processing and functional defects of cystic fibrosis transmembrane conductance regulator delta f508.
Volume: 277
Issue: 39
Pages: 35896-905
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Publication
7537458 | J:24488
First Author: De Lisle RC
Year: 1995
Journal: Am J Physiol
Title: Increased expression of sulfated gp300 and acinar tissue pathology in pancreas of CFTR(-/-) mice.
Volume: 268
Issue: 4 Pt 1
Pages: G717-23
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Publication
12461646 | J:80597
First Author: Haston CK
Year: 2002
Journal: Mamm Genome
Title: Mapping of genetic factors influencing the weight of cystic fibrosis knockout mice.
Volume: 13
Issue: 11
Pages: 614-8
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Publication
14529837 | J:101822
First Author: Ostrowski LE
Year: 2003
Journal: Mol Ther
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